6533b82dfe1ef96bd1292000

RESEARCH PRODUCT

Cholesteatoma of the hypotympanum in a patient with Treacher Collins syndrome

Dimitrios KoutsimpelasWolf J. MannSusanne WriedtBilal Al NawasSophie Mann

subject

Malemedicine.medical_specialtyAdolescentHypotympanotomyOpen cavityEar MiddlemedicineHumansCholesteatoma Middle Earbusiness.industryCholesteatomaGeneral Medicinemedicine.diseaseJugular paragangliomaMagnetic Resonance ImagingSurgerymedicine.anatomical_structureOtorhinolaryngologyMiddle earSurgeryTomography X-Ray ComputedbusinessTreacher Collins syndromeMandibulofacial DysostosisJugular foramenPreoperative imaging

description

In the present article we report a cholesteatoma of the hypotympanum extending to the jugular foramen in a 16-year-old male with Treacher Collins syndrome. Preoperative imaging excluded jugular paraganglioma and set the diagnosis of cholesteatoma. We discuss the operative treatment via a large hypotympanotomy and creation of an open hypotympanic cavity. To the authors' knowledge this is the first description of hypotympanal cholesteatoma with such an extension, being treated through this approach.

yearjournalcountryeditionlanguage
2014-02-01Auris Nasus Larynx
https://doi.org/10.1016/j.anl.2013.05.005