6533b832fe1ef96bd129a2d8
RESEARCH PRODUCT
Dystrophic epidermolysis bullosa: oral findings and problems.
Brita WillershausenChristiane GleissnerLudwig HofmannBirgül AzrakKristina Kaevelsubject
MalePit and Fissure SealantsToothbrushingmedicine.medical_specialtyMouthwashesDiseaseDental CariesOral hygieneGingivitismedicineHumansChildDental Restoration PermanentGeneral Dentistrybusiness.industryMicrostomiaDental Care for DisabledChlorhexidineChlorhexidineEpidermolysis bullosa dystrophicamedicine.diseaseDental Care for DisabledDermatologyEpidermolysis Bullosa Dystrophicastomatognathic diseasesTooth ExtractionAnti-Infective Agents LocalEpidermolysis bullosamedicine.symptombusinessmedicine.drugFollow-Up Studiesdescription
Dystrophic epidermolysis bullosa (DEB) is one of the three major types of epidermolysis bullosa (EB), an inherited cutaneous disease with blister formation following minor trauma. A subtype of DEB is recessive dystrophic epidermolysis bullosa, Hallopeau-Siemens type (RDEB-HS), where marked scarring leads to deformities of extremities. In RDEB-HS the mucous membranes may also be involved and form adhesions with ankyloglossia and microstomia. Oral hygiene is difficult. A 7-year-old boy with RDEB-HS was brought to the Johannes Gutenberg University dental clinic with dental pain. He had multiple carious lesions, poor oral hygiene and gingivitis. Because he was noncompliant and had microstomia, he required dental therapy under general anesthesia. The recall visits over the past two years had demonstrated that the dental health of this patient with RDEB-HS could be maintained by means of improved oral home care, using antibacterial agents.
| year | journal | country | edition | language |
|---|---|---|---|---|
| 2006-05-01 | Special care in dentistry : official publication of the American Association of Hospital Dentists, the Academy of Dentistry for the Handicapped, and the American Society for Geriatric Dentistry |