Search results for " PI"

showing 10 items of 6620 documents

Mutational screening of the USH2A gene in Spanish USH patients reveals 23 novel pathogenic mutations

2011

Abstract Background Usher Syndrome type II (USH2) is an autosomal recessive disorder, characterized by moderate to severe hearing impairment and retinitis pigmentosa (RP). Among the three genes implicated, mutations in the USH2A gene account for 74-90% of the USH2 cases. Methods To identify the genetic cause of the disease and determine the frequency of USH2A mutations in a cohort of 88 unrelated USH Spanish patients, we carried out a mutation screening of the 72 coding exons of this gene by direct sequencing. Moreover, we performed functional minigene studies for those changes that were predicted to affect splicing. Results As a result, a total of 144 DNA sequence variants were identified.…

AdultMaleSequence VariantsAdolescentGenotypegenetic structuresUsher syndromeDNA Mutational AnalysisMutation Missenselcsh:MedicineBiologymedicine.disease_causeExonYoung AdultUSH2ARetinitis pigmentosaGenotypemedicineotorhinolaryngologic diseasesHumansGenetics(clinical)Pharmacology (medical)<it>USH2A</it>GeneAllele frequencyGenetics (clinical)GeneticsMedicine(all)MutationExtracellular Matrix ProteinsResearchlcsh:RGeneral MedicineExonsMiddle Agedmedicine.diseaseeye diseasesPhenotypeSpainMutationFemalesense organsUsher SyndromeUsher SyndromesMutationsMinigeneOrphanet Journal of Rare Diseases
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Study of lip hydration with application of photoprotective lipstick : influence of skin phototype, size of lips, age, sex and smoking habits

2009

Objectives: To study lip hydration levels when applying a lipstick sunscreen for 3 months and to evaluate the influence of size of lips, age, sex, smoking and skin phototype. Study design: The study group was formed by 140 volunteer subjects, one group consisting of 70 patients applying a commercial lipstick sunscreen three times a day and the other group of 70 controls in which no product was applied. The age range was 20-86 years. The influence in lip hydration levels of age, sex, phototype, size of the lips and smoking habits was studied using a Corneometer 825® (Courage and Khazaka Electronic GmbH, Cologne, Germany). Results: An increase in lip hydration was found between the basal (53.…

AdultMaleSmoking habitDentistrySkin PigmentationCosmeticsYoung AdultSex FactorsBody WaterSex factorsMedicineHumansGeneral DentistryVolunteerAgedAged 80 and overbusiness.industrySmokingAge FactorsOrgan SizeLipstickMiddle Aged:CIENCIAS MÉDICAS [UNESCO]PhototypeLipstomatognathic diseasesOtorhinolaryngologyUNESCO::CIENCIAS MÉDICASSurgeryFemalebusinessSunscreening Agents
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Trends and Prevalence of Nocturia Among US Adults, 2005-2016

2019

Purpose: Increased nocturia episodes can be a clinical marker of poor health status. The present study aimed to evaluate patterns and temporal trends in nocturia and sociodemographic and lifestyle correlates in the US population. Methods: Participants, aged 20 years or older, were included in this repeated cross-sectional study. The National Health and Nutrition Examination Survey from 2005 to 2016 was used. Participants were asked “During the past 30 days, how many times per night did you most typically get up to urinate, from the time you went to bed at night until the time you got up in the morning?”. Individuals were categorized as either ≥ 1 nocturia episode or ≥ 2 nocturia episodes pe…

AdultMaleTime FactorsNational Health and Nutrition Examination SurveyUrologymedia_common.quotation_subjectPopulation030232 urology & nephrologyClinical marker030204 cardiovascular system & hematologyUrination03 medical and health sciencesYoung AdultSoysal P. Cao C. Xu T. Yang L. Isik A. Turan K. Liu Q. Pizzol D. Veronese N. Demurtas J. et al. -Trends and prevalence of nocturia among US adults 2005-2016.- International urology and nephrology 20190302 clinical medicineAge groupsPrevalenceMedicineNocturiaHumanseducationNocturia · Trend · United States · NHANESMorningmedia_commoneducation.field_of_studybusiness.industryMiddle AgedUnited StatesSecular variationCross-Sectional StudiesNephrologyFemaleNocturiamedicine.symptombusinessDemography
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Studies on the subcellular pathophysiology of sublethal chronic cell injury.

1974

Summary This paper summarizes some of the important subcellular events occurring after chronic sublethal cell injury. Chronic cell injury is defined as the result of injurious stimuli which permit cell survival though in altered steady states for protracted periods of time. The importance of ultrastructural and biochemical studies of these phenomena is emphasized. Among the phenomena discussed are alterations in lysosomes, cellular hypertrophy, fatty metamorphosis, alterations in microfilaments and microtubules, alterations in mechanisms of transcription and replication, disturbances in the cell surface and transport across the cell membrane, and alterations in intracellular transport.

AdultMaleTime FactorsTranscription GeneticSurface PropertiesCellsCellGuinea PigsBronchiBiologyMicrofilamentMicrotubulesPathology and Forensic MedicineMuscle hypertrophyCell Physiological PhenomenaCell membraneMiceMicrotubuleTranscription (biology)medicineAnimalsHumansCerebral CortexMacrophagesMusclesCell MembraneBiological TransportGeneral MedicineHypertrophyMiddle AgedPathophysiologyCell biologyMicroscopy Electronmedicine.anatomical_structureLiverUltrastructureRabbitsLysosomesCell DivisionBeitrage zur Pathologie
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Aqueous Humor Levels of Vascular Endothelial Growth Factor in Retinitis Pigmentosa

2008

PURPOSE To determine the level of vascular endothelial growth factor A (VEGF-A) in aqueous humors of patients with retinitis pigmentosa (RP). METHODS A prospective, comparative control study. Aqueous humor was collected from 16 eyes of 16 patients with RP. The level of VEGF-A was determined with a commercially available enzyme-linked immunosorbent assay kit. The control group comprised 16 aqueous samples from 16 patients about to undergo cataract surgery and without any other ocular or systemic diseases. RESULTS The concentration of VEGF-A in aqueous humor was markedly lower in patients with RP than in control subjects (Mann-Whitney U test, P < 0.001). The level of VEGF-A was 94.9 +/- 99.8 …

AdultMaleVascular Endothelial Growth Factor Amedicine.medical_specialtygenetic structuresmedicine.medical_treatmentEye diseaseEnzyme-Linked Immunosorbent AssayAqueous humorAqueous Humorchemistry.chemical_compoundOphthalmologyRetinitis pigmentosaHumansMedicineProspective StudiesAgedbusiness.industryMiddle AgedCataract surgerymedicine.diseaseControl subjectseye diseasesVascular endothelial growth factorVascular endothelial growth factor AchemistryFemalesense organsbusinessRetinitis PigmentosaRetinopathyInvestigative Opthalmology &amp; Visual Science
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The Auditory Kuleshov Effect: Multisensory Integration in Movie Editing

2016

Almost a hundred years ago, the Russian filmmaker Lev Kuleshov conducted his now famous editing experiment in which different objects were added to a given film scene featuring a neutral face. It is said that the audience interpreted the unchanged facial expression as a function of the added object (e.g., an added soup made the face express hunger). This interaction effect has been dubbed “Kuleshov effect.” In the current study, we explored the role of sound in the evaluation of facial expressions in films. Thirty participants watched different clips of faces that were intercut with neutral scenes, featuring either happy music, sad music, or no music at all. This was crossed with the facia…

AdultMaleVisual perceptionEmotionsMotion PicturesFace (sociological concept)Experimental and Cognitive PsychologyFilm editing050105 experimental psychologyYoung Adult03 medical and health sciences0302 clinical medicineArtificial IntelligenceHumans0501 psychology and cognitive sciencesFacial expression05 social sciencesMultisensory integrationObject (philosophy)Sensory SystemsFacial ExpressionOphthalmologyAcoustic StimulationAuditory PerceptionVisual PerceptionFilm directorFemalePsychologyMusicPhotic Stimulation030217 neurology & neurosurgeryMeaning (linguistics)Cognitive psychologyPerception
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The big picture: effects of surround on immersion and size perception.

2014

Despite the fear of the entertainment industry that illegal downloads of films might ruin their business, going to the movies continues to be a popular leisure activity. One reason why people prefer to watch movies in cinemas may be the surround of the movie screen or its physically huge size. To disentangle the factors that might contribute to the size impression, we tested several measures of subjective size and immersion in different viewing environments. For this purpose we built a model cinema that provided visual angle information comparable with that of a real cinema. Subjects watched identical movie clips in a real cinema, a model cinema, and on a display monitor in isolation. Wher…

AdultMaleVisual perceptionMotion PicturesEntertainment industryExperimental and Cognitive PsychologyVisual artsMovie theaterYoung AdultContextual designArtificial IntelligenceHumansGeneralLiterature_REFERENCE(e.g.dictionariesencyclopediasglossaries)Size PerceptionAnalysis of Variancebusiness.industryViewing angleSensory SystemsOphthalmologyDisplay sizeFemaleSize PerceptionVisual anglePsychologybusinessPhotic StimulationPerception
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Methodological Aspects of the Application of the Naka-Rushton Equation to Clinical Electroretinogram

1993

The nonlinear relation between stimulus intensity and response amplitude of the electroretinogram (ERG) scotopic b wave can be described by a curve based on the Naka-Rushton (NR) equation. Up to now, the NR equation has been used to assess the features of the normal and pathological ERG, but the best approach for a correct evaluation of the parameters is still debatable. The parameters are thought to be related to the different conditions of retinal activities. The method is well known in experimental laboratories but is quite unusual at the clinical level. In the present paper the derivative analysis of the NR function is proposed as an easier approach to understand the variations of the N…

AdultMaleX ChromosomeAdolescentLightElectrodiagnosisGenetic LinkageVisual AcuityDark AdaptationCataractRetinaCellular and Molecular NeuroscienceExperimental LaboratoriesOpticsRetinal DiseasesElectroretinographymedicineHumansResponse AmplitudeApplied mathematicsScotopic visionChildAgedMathematicsmedicine.diagnostic_testbusiness.industryDerivative analysisGeneral MedicineMiddle AgedSensory SystemsOphthalmologyFemalebusinessRetinitis PigmentosaElectroretinographyOphthalmic Research
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Evidence of noncentrosymmetry of human tooth hydroxyapatite crystals

2014

Herein, we investigate human single hydroxyapatite crystals (enamel and dentine) by convergent-beam electron diffraction (CBED) and automated electron-diffraction tomography (ADT). The CBED pattern shows the absence of the mirror plane perpendicular to the c axis leading to the P63 space group instead of the P63 /m space group considered for larger-scale crystals, this is confirmed by ADT. This experimental evidence is of prime importance for understanding the morphogenesis and the architectural organization of calcified tissues.

AdultMaleatomic structuresCatalysisX-Ray DiffractionHuman toothmedicineHydroxidesHumansDental Enamelatomic structures; biomineralization; human tooth crystals; noncentrosymmetry; piezoelectricityEnamel paintpiezoelectricityChemistryOrganic ChemistrySpectrometry X-Ray EmissionGeneral Chemistrybiomineralizationnoncentrosymmetrystomatognathic diseasesCrystallographymedicine.anatomical_structureDurapatiteElectron diffractionvisual_artDentinvisual_art.visual_art_mediumNanoparticleshuman tooth crystalsFemaleMirror plane
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The neuroendocrinological profile of roxindole, a dopamine autoreceptor agonist, in schizophrenic patients

1995

Roxindole is a potent autoreceptor-selective dopamine agonist with additional properties as a serotonin reuptake inhibitor and 5-HT1A agonist. In order to get more insight into its mode of action in various psychiatric populations, we evaluated the effects of subchronic roxindole treatment on pituitary and adrenal hormone secretion, i.e. release of prolactin, thyroid stimulating hormone (TSH), growth hormone (GH), luteinizing hormone (LH), and cortisol. Fifteen schizophrenic patients with positive and negative symptomatology, respectively, were treated with roxindole for 28 days. Both basal and thyrotropin releasing hormone (TRH) -induced prolactin secretion diminished significantly to 26.4…

AdultMaleendocrine systemmedicine.medical_specialtyIndolesHydrocortisoneendocrine system diseasesPyridinesThyrotropinThyrotropin-releasing hormonePharmacologyDopamine agonistchemistry.chemical_compoundThyroid-stimulating hormoneAnterior pituitaryRoxindoleInternal medicinemedicineHumansPharmacologybusiness.industryLuteinizing HormoneMiddle AgedProlactinGrowth hormone secretionOxindolesProlactinEndocrinologymedicine.anatomical_structurechemistryGrowth HormoneDopamine AgonistsSchizophreniaFemaleSchizophrenic PsychologyLuteinizing hormonebusinesshormones hormone substitutes and hormone antagonistsmedicine.drugPsychopharmacology
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