Search results for "39"
showing 10 items of 1787 documents
Sturge-Weber syndrome: a report of 14 cases
2013
Sturge-Weber-Krabe syndrome (SWS), also known as encephalotrigeminalangiomatosis and named the forthfacomatosis, recall the names of the authors who first describedit in its basic clinical, radiological andanatomopathological aspects. We report here 14 cases of Sturge-Weber disease. In 6 of these, despite what had been previously described in literature, an extension of the angioma has been noted in other parts of the body. The study of these subjects stresses not only the need for a pharmacological/neuropsychomotor intervention, but alsothe need of a psychotherapeutic approach, for the emotional and affective implications thatcould derive from this syndrome. The reported cases are similar …
On new means with interesting practical applications: Generalized power means
2021
Means of positive numbers appear in many applications and have been a traditional matter of study. In this work, we focus on defining a new mean of two positive values with some properties which are essential in applications, ranging from subdivision and multiresolution schemes to the numerical solution of conservation laws. In particular, three main properties are crucial—in essence, the ideas of these properties are roughly the following: to stay close to the minimum of the two values when the two arguments are far away from each other, to be quite similar to the arithmetic mean of the two values when they are similar and to satisfy a Lipchitz condition. We present new means with these pr…
Voice and authorial body in Juana Manso
2021
El estilo de Juana Manso fue calificado por Sarmiento como «escandaloso». Esa manera inequívoca de presentarse públicamente delimitó desde entonces un modo de existencia, de circulación y de funcionamiento de su figura autorial en el campo cultural argentino de mediados de siglo XIX. Este artículo se propone rastrear esta singular «puesta en escena» de la escritora como un dispositivo de enunciación que no se limita a sus textos, en la doble dimensión que ocupa, como autora y como actora de ese campo. ¿Cómo se construye, en esta puesta escena, su voz y su imagen?, ¿Cómo se difunde ese cuerpo de autora? En la conjunción de género y profesión, la función-Manso se concreta en un tono de escrit…
THERAPEUTIC EFFICACY OF MAGNESIUM VALPROATE IN SUCCINIC SEMIALDEHYDE DEHYDROGENASE DEFICIENCY
2012
Succinic semialdehyde dehydrogenase deficiency (SSADHD or gammahydroxybutyric aciduria), a disorder of γ-aminobutyric acid (GABA) metabolism, manifests as a slowly progressive or static encephalopathy. The latter encompasses prominent cognitive dysfunction, neuropsychiatric morbidity and epilepsy.We report safe and effective treatment with MgVPA in an adolescent female with SSADHD and seizures refractory to a broad spectrum of antiepileptics. MgVPA therapy (20 mg/Kg/day) was introduced at 7 years based upon behavioural difficulties and EEG alterations without adverse effects. Therapy was halted at age 13 years, and reintroduced at 14 years, due to new onset complex partial seizures. EEG dem…
Tendencies in ABO3 Perovskite and SrF2, BaF2 and CaF2 Bulk and Surface F-Center Ab Initio Computations at High Symmetry Cubic Structure
2021
This research was partly funded by the Latvian Council of Science project No. LZP‐ 2020/2‐0009 (for R. Eglitis), as well as the ERAF Project No. 1.1.1.1/18/A/073. We express our gratitude for the financial support from Latvian–Ukraine cooperation Project No. Latvia–Ukraine LV‐ UA/2021/5. The Institute of Solid State Physics, University of Latvia (Latvia), as the Centre of Excellence has received funding from the European Unions Horizon 2020 Framework Pro‐ gramme H2020‐WIDESPREAD01‐2016‐2017‐Teaming Phase2 under Grant Agreement No. 739508, project CAMART2.
Sustainable Development Model of EU Cities Compliant with UN Settings
2021
Nowadays, the globally accepted UN concept of sustainable development (SD) is gradu®ally transferred to the city level, including small and medium-sized cities. The implementation of SD settings requires regular measurement of developmental progress to monitor the level achieved in statics and dynamics, and to make strategic decisions for the next period. The existing urban SD indicator systems and indices are not well-suited for the monitoring of specific cities. Benchmarking algorithms and mathematical modelling procedures were applied to create a methodology and mathematical model for measuring the achieved urban SD level and to ensure the most objective selection and proportions of key …
Visual Discrimination of the 17 Plane Symmetry Groups
2011
Within most of the 17 plane symmetry groups, individual symmetry operations act in multiple, nonequivalent ways. This, and the fact that many groups can be realized on the basis of different unit cells and generating regions, poses difficulties for visual discrimination and identification. Because of inherent confounds, only few of the groups can be studied by traditional experimental methodology. The use of an oddity paradigm and specific tiling patterns that camouflage groups in complex textures are recommended as partial remedy to this impasse. In order to prepare readers for an appreciation of the aforementioned issues and to provide a rationale for their investigation, the reporting of…
Estimation of the spatially distributed surface energy budget for AgriSAR 2006, part I : remote sensing model intercomparison
2011
A number of energy balance models of variable complexity that use remotely sensed boundary conditions for producing spatially distributed maps of surface fluxes have been proposed. Validation typically involves comparing model output to flux tower observations at a handful of sites, and hence there is no way of evaluating the reliability of model output for the remaining pixels comprising a scene. To assess the uncertainty in flux estimation over a remote sensing scene requires one to conduct pixel-by-pixel comparisons of the output. The objective of this paper is to assess whether the simplifications made in a simple model lead to erroneous predictions or deviations from a more complex mod…
Hepatitis C virus and cardiovascular: A review
2017
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Autoroutes, activités et territoires: propositions méthodologiques pour évaluer l'impact de l'autoroute sur la spatialisation des activités
2003
International audience; L'autoroute est-elle capable de fixer les activités ? Cette question relativement simple, ancienne etcontroversée, posée par la Société des Autoroutes Paris-Rhin-Rhône n'a toujours pas été résolue malgrél'acceptation d'une logique d'interactions primant sur une logique d'effets automatiques d'un seul élément. Ellese heurte essentiellement à un blocage méthodologique qui empêche, en l'état actuel des recherches, d'yrépondre de manière plus rigoureuse et d'exporter des conclusions validées dans tous les cas. Aussi, nousproposons une nouvelle méthode de recherche qui intègre la totalité du système de localisation des activités etune nouvelle conception de recherche qui …