Search results for "870"

showing 10 items of 116 documents

Early-infantile onset epilepsy and developmental delay caused by bi-allelic GAD1 variants

2020

Mice lacking GAD1 show neonatal mortality, but the human phenotype associated with GAD1 disruption is poorly characterized. Neuray et al. describe six patients with biallelic GAD1 mutations, presenting with early-infantile onset epilepsy, neurodevelopmental delay, muscle weakness and non-CNS manifestations.

Male0301 basic medicineGlutamate decarboxylaseMalalties cerebralsNeurotransmissorsNeurodevelopmental delayEpilepsy0302 clinical medicineMESH: ChildAge of OnsetChildcleft palateGAD1AcademicSubjects/SCI01870Glutamate DecarboxylaseGlutamate receptorMuscle weakness//purl.org/becyt/ford/3.1 [https]NeurotransmittersMESH: InfantHypotoniamuscle weakneCleft palateMESH: EpilepsyChild PreschoolMuscle Hypotonia[SDV.NEU]Life Sciences [q-bio]/Neurons and Cognition [q-bio.NC]//purl.org/becyt/ford/3 [https]FemaleBrain diseasesAbnormalitiesmedicine.symptomMultiplemedicine.drugcleft palate; epilepsy; GAD1; muscle weakness; neurodevelopmental delayMESH: Glutamate Decarboxylasemedicine.medical_specialtyMESH: Abnormalities MultipleMESH: MutationMESH: Age of OnsetBiologyInhibitory postsynaptic potentialGAD1 cleft palate epilepsy muscle weakness neurodevelopmental delay.gamma-Aminobutyric acidGAD1neurodevelopmental delay03 medical and health sciencesExcitatory synapseInternal medicinemedicineHumansAbnormalities MultiplePreschoolAllelesMESH: Neurodevelopmental Disordersmuscle weaknessMESH: HumansEpilepsyMESH: Muscle HypotoniaMESH: AllelesMESH: Child PreschoolInfantmedicine.diseaseMESH: MaleEpilèpsiaEditor's Choice030104 developmental biologyEndocrinologyNeurodevelopmental DisordersMutationepilepsyAcademicSubjects/MED00310Neurology (clinical)Cleft palate; Epilepsy; GAD1; Muscle weakness; Neurodevelopmental delay; Abnormalities Multiple; Age of Onset; Alleles; Child; Child Preschool; Epilepsy; Female; Glutamate Decarboxylase; Humans; Infant; Male; Muscle Hypotonia; Mutation; Neurodevelopmental DisordersMESH: Female[SDV.MHEP]Life Sciences [q-bio]/Human health and pathology030217 neurology & neurosurgeryReports
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Spermiogram and sperm head morphometry assessed by multivariate cluster analysis results during adolescence (12-18 years) and the effect of varicocele

2016

Artículo científico This work evaluates sperm head morphometric characteristics in adolescents from 12 to 18 years of age, and the effect of varicocele. Volunteers between 150 and 224 months of age (mean 191, n = 87), who had reached oigarche by 12 years old, were recruited in the area of Barranquilla, Colombia. Morphometric analysis of sperm heads was performed with principal component (PC) and discriminant analysis. Combining seminal fluid and sperm parameters provided five PCs: two related to sperm morphometry, one to sperm motility, and two to seminal fluid components. Discriminant analysis on the morphometric results of varicocele and nonvaricocele groups did not provide a useful class…

Male0301 basic medicineMultivariate statisticsMultivariate analysisVaricocelelcsh:RC870-923:MEDICINE::Morphology cell biology pathology [Research Subject Categories]0302 clinical medicineVaricoceleCluster AnalysisChildsubpopulationreproductive and urinary physiologySperm motilityeducation.field_of_study030219 obstetrics & reproductive medicinemedicine.diagnostic_testGeneral MedicineSpermatozoaseminal qualitySperm MotilityCASA-Morph systemSecrecionesendocrine systemAdolescentUrologyPopulationInvited Original ArticleSemen analysisBiologyDisease clusterAndrology03 medical and health sciencesFluidosmedicineHumansadolescence; CASA-Morph system; seminal quality; sperm head morphometry; spermiogram; subpopulationeducationCell Shapeurogenital systemlcsh:Diseases of the genitourinary system. Urologymedicine.diseasespermiogramGenéticaSpermSemen Analysis030104 developmental biologyMultivariate AnalysisAdolescenciaSperm Headadolescencesperm head morphometryAsian Journal of Andrology
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Human brain ages with hierarchy-selective attenuation of prediction errors

2020

Abstract From the perspective of predictive coding, our brain embodies a hierarchical generative model to realize perception, which proactively predicts the statistical structure of sensory inputs. How are these predictive processes modified as we age? Recent research suggested that aging leads to decreased weighting of sensory inputs and increased reliance on predictions. Here we investigated whether this age-related shift from sensorium to predictions occurs at all levels of hierarchical message passing. We recorded the electroencephalography responses with an auditory local–global paradigm in a cohort of 108 healthy participants from 3 groups: seniors, adults, and adolescents. The detect…

MaleMismatch negativityAudiologyElectroencephalographyRandom Allocation[SCCO]Cognitive scienceCognition0302 clinical medicineprediction errorsEEGelectroencephalography (EEG)predictive codingmedia_commonAged 80 and overmedicine.diagnostic_testAcademicSubjects/SCI0187005 social sciencesBrainElectroencephalographyMiddle Agedhavaintopsykologiaauditory perceptionEvoked Potentials AuditoryOriginal ArticleFemalePsychologyAdultAuditory perceptionmedicine.medical_specialtyCognitive Neurosciencemedia_common.quotation_subjectSensory systemkuulohavainnot050105 experimental psychologyYoung Adult03 medical and health sciencesCellular and Molecular NeuroscienceP3aPerceptionP3bmedicineHumans0501 psychology and cognitive sciencesAcademicSubjects/MED00385AgedWorking memory[SCCO.NEUR]Cognitive science/NeuroscienceaginghavainnotikääntyminenAcoustic StimulationAcademicSubjects/MED00310Psychomotor Performance030217 neurology & neurosurgeryForecasting
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Comparison of different statistical approaches to evaluate morphometric sperm subpopulations in men.

2016

This study was designed to characterize morphometric sperm subpopulations in normozoospermic men by using different statistical methods and examining their suitability to classify correctly different sperm nuclear morphologies present in human ejaculates. Ejaculates from 21 normozoospermic men were collected for the study. After semen collection and analysis, samples were prepared for morphometric determination. At least 200 spermatozoa per sample were assessed for sperm morphometry by computer-assisted sperm morphometry analysis (CASA-Morph) using fluorescence. Clustering and discriminant procedures were performed to identify sperm subpopulations from the morphometric data obtained. Cluste…

MaleMultivariate statisticsendocrine systemUrologyInvited Original ArticleBiologylcsh:RC870-923Semen collectionCell sizeAndrology03 medical and health sciences0302 clinical medicinemanCluster AnalysisHumansCell Shapereproductive and urinary physiologyCell SizePrincipal Component Analysis030219 obstetrics & reproductive medicineurogenital system0402 animal and dairy science04 agricultural and veterinary sciencesGeneral Medicinelcsh:Diseases of the genitourinary system. Urology040201 dairy & animal scienceSpermSpermatozoaNuclear shapeSemen AnalysisPrincipal component analysissperm subpopulationscomputer-assisted sperm morphometry analysis; man; sperm subpopulationscomputer-assisted sperm morphometry analysisAsian journal of andrology
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Cardiovascular risk factors and the impact on prognosis in patients with chronic kidney disease secondary to autosomal dominant polycystic kidney dis…

2021

Background: Autosomal dominant polycystic kidney disease (ADPKD) is the most frequent hereditary renal disease. There is an increased rate of cardiovascular disease (CVD) in ADPKD. In this study, we evaluate the prevalence of cardiovascular risk factors, the achievement rates for treatment goals and cardiovascular events (CVE) in ADPKD and their relations with asymptomatic CVD in CKD from other etiologies (CKDoe) and controls. Methods: We evaluated 2445 CKD patients (2010–2012). The information collected was: clinical, anthropometric and analytical parameters, treatments and CVD evaluation (intima-media thickness (IMT), atheromatous plaque presence and ankle-brachial index (ABI)). Laborator…

MaleNephrologymedicine.medical_specialtyAutosomal dominant polycystic kidney diseaseRenal functionComorbiditylcsh:RC870-923urologic and male genital diseasesCarotid Intima-Media ThicknessAsymptomaticNephropathyAutosomal dominant polycystic kidney diseaseInternal medicineChronic kidney diseasemedicineHumansAnkle Brachial Indexcardiovascular diseasesRenal Insufficiency ChronicProteinuriabusiness.industryMiddle AgedPolycystic Kidney Autosomal DominantPrognosislcsh:Diseases of the genitourinary system. Urologymedicine.diseaseCardiovascular diseasePlaque Atheroscleroticfemale genital diseases and pregnancy complicationsNephropathyCor MalaltiesBlood pressureCardiovascular DiseasesHeart Disease Risk FactorsNephrologyDisease ProgressionInsuficiència renal crònicaFemalemedicine.symptombusinessResearch ArticleKidney disease
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Characterization of human infiltrating and circulating gamma-delta T cells in prostate cancer

2019

Purpose The aim of our study was to prospectively evaluate the distribution of gamma-delta (γδ)1 and γδ2 T cells and their phenotypes in peripheral blood and prostate samples of patients diagnosed with or without prostate cancer (PCa) at prostate biopsy. Materials and methods A consecutive series of 43 outpatients underwent trans-rectal echo-guided prostate biopsy for suspected PCa. Flow cytometry analysis was used to identify and characterize the γδ T cells populations in peripheral blood and tissue samples. Patients were stratified according to the presence or not of PCa, and its International Society of Urological Pathology (ISUP) grade (1 vs. ≥2). Results The distribution of γδ T cells …

MalePathologymedicine.medical_specialtyProstate biopsyT-Lymphocyte subsetUrological OncologyBiopsyUrology030232 urology & nephrologylcsh:RC870-923Flow cytometry03 medical and health sciencesProstate cancerLymphocytes Tumor-Infiltrating0302 clinical medicineProstateBiopsymedicineHumansProspective StudiesIntraepithelial LymphocytesAgedNeoplasm gradingmedicine.diagnostic_testbusiness.industryCancerMiddle AgedNeoplastic Cells Circulatinglcsh:Diseases of the genitourinary system. Urologymedicine.diseasePhenotypeImmunologic surveillanceImmunosurveillancemedicine.anatomical_structure030220 oncology & carcinogenesisOriginal ArticleProstatic neoplasmsProstatic neoplasmbusinessT-Lymphocyte subsetsInvestigative and Clinical Urology
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Sexual dysfunctions after transurethral resection of the prostate (TURP): evidence from a retrospective study on 264 patients

2015

Objectives: Benign prostatic hyperplasia (BPH) and sexual dysfunctions are diseases with a high prevalence in aged men. Several studies have found a link between BPH and LUTS resulting from deterioration in sexual function in men aged 50 years and older for whom TURP is considered the gold standard. The impact of TURP on sexual functions still remain uncertain, nor is it clear what pathophysiological mechanism underlying the emergence of new episodes of Erectile Dysfunction (ED) following TURP in patients with normal sexual function before surgery, while retrograde ejaculation and ejaculate volume reduction represent a clear side effect; derived from BPH treatment. The aim of this study was…

MaleRetrograde ejaculationmedicine.medical_specialtyLongitudinal studyUrologymedicine.medical_treatmentProstatic Hyperplasialcsh:RC870-923urologic and male genital diseasesPreoperative careSettore MED/24 - UrologiaErectile DysfunctionErectile Dysfunction (ED)Surveys and QuestionnairesInternal medicinePreoperative CaremedicineHumansInternational index of erectile function (IIEF)Longitudinal StudiesSicilyTransurethral resection of the prostate (TURP)AgedRetrospective StudiesTransurethral resection of the prostateAged 80 and overPostoperative CareLibidoBenign prostatic hyperplasiabusiness.industryBenign prostatic hyperplasia (BPH)Low urinary tract symptoms (LUTS).Transurethral Resection of ProstateTransurethral resection of the prostateRetrospective cohort studyMiddle Agedlcsh:Diseases of the genitourinary system. Urologymedicine.diseaseInternational index of erectile functionLow urinary tract symptomsSurgeryErectile dysfunctionSexual functionbusinessArchivio Italiano di Urologia e Andrologia
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Computer-assisted sperm morphometry fluorescence-based analysis has potential to determine progeny sex

2016

This study was designed to determine the ability of computer-assisted sperm morphometry analysis (CASA-Morph) with fluorescence to discriminate between spermatozoa carrying different sex chromosomes from the nuclear morphometrics generated and different statistical procedures in the bovine species. The study was divided into two experiments. The first was to study the morphometric differences between X- and Y-chromosome-bearing spermatozoa (SX and SY, respectively). Spermatozoa from eight bulls were processed to assess simultaneously the sex chromosome by FISH and sperm morphometry by fluorescence-based CASA-Morph. SX cells were larger than SY cells on average (P < 0.001) although with impo…

MaleSex Determination Analysisendocrine systemUrology[SDV]Life Sciences [q-bio]SemenInvited Original ArticleSexingSemen analysisBiologylcsh:RC870-923mammalian spermotozoasperm morphometryAndrology03 medical and health sciencesbull; computer-assisted sperm morphometry analysis; sexing; sperm morphometry0302 clinical medicineDiscriminant function analysismedicineAnimalssexingbullCell Shapereproductive and urinary physiologyx-chromosome-bearingnuclear shapeCell NucleusMorphometrics030219 obstetrics & reproductive medicinemedicine.diagnostic_testurogenital system0402 animal and dairy scienceChromosome04 agricultural and veterinary sciencesGeneral MedicineAnatomylcsh:Diseases of the genitourinary system. UrologySpermatozoa040201 dairy & animal scienceSpermSemen AnalysisMicroscopy FluorescenceSex Determination AnalysisCattlex-chromosome-bearing;mammalian spermotozoa;nuclear shapecomputer-assisted sperm morphometry analysis
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Morphometry and subpopulation structure of Holstein bull spermatozoa: variations in ejaculates and cryopreservation straws

2016

Artículo científico Sperm quality is evaluated for the calculation of sperm dosage in artificial reproductive programs. The most common parameter used is motility, but morphology has a higher potential as a predictor of genetic quality. Morphometry calculations from CASA‑Morph technology improve morphological evaluation and allow mathematical approaches to the problem. Semen from 28 Holstein bulls was collected by artificial vagina, and several ejaculates were studied. After general evaluation, samples were diluted, packaged in 0.25 ml straws, and stored in liquid nitrogen. Two straws per sample were thawed, and slides were processed and stained with Diff‑Quik. Samples were analyzed by a CA…

Maleanimal structuresHolstein bullUrologymedicine.medical_treatmentPopulationSemenInvited Original ArticleTotal populationBiologylcsh:RC870-923Cryopreservationsperm morphometry03 medical and health sciences0302 clinical medicineAnimal sciencemedicineAnimalsMorfologíaeducationsubpopulationsDairy cattle:FORESTRY AGRICULTURAL SCIENCES and LANDSCAPE PLANNING::Plant production::Agronomy [Research Subject Categories]CryopreservationMorphometricseducation.field_of_study030219 obstetrics & reproductive medicineArtificial insemination0402 animal and dairy science04 agricultural and veterinary sciencesGeneral MedicineReproducciónlcsh:Diseases of the genitourinary system. UrologySpermatozoaGenética040201 dairy & animal scienceSpermSemen AnalysisMortalidadSperm Motilitycryopreservation; Holstein bull; sperm morphometry; subpopulationsCattleSemen PreservationAsian Journal of Andrology
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Sperm kinematic, head morphometric and kinetic-morphometric subpopulations in the blue fox (Alopex lagopus)

2016

This work provides information on the blue fox ejaculated sperm quality needed for seminal dose calculations. Twenty semen samples, obtained by masturbation, were analyzed for kinematic and morphometric parameters by using CASA-Mot and CASA-Morph system and principal component (PC) analysis. For motility, eight kinematic parameters were evaluated, which were reduced to PC1, related to linear variables, and PC2, related to oscillatory movement. The whole population was divided into three independent subpopulations: SP1, fast cells with linear movement; SP2, slow cells and nonoscillatory motility; and SP3, medium speed cells and oscillatory movement. In almost all cases, the subpopulation dis…

Maleendocrine systemUrologyPopulationFoxesMotilitySemenInvited Original ArticleKinematicsBiologyintegration of motility and morphologylcsh:RC870-923Sperm Preservationsperm morphometry03 medical and health sciences0302 clinical medicineAnimalseducationCell ShapesubpopulationSperm motilityPrincipal Component Analysiseducation.field_of_study030219 obstetrics & reproductive medicine0402 animal and dairy scienceintegration of motility and morphology; principal component analysis; sperm morphometry; subpopulation04 agricultural and veterinary sciencesGeneral MedicineAnatomylcsh:Diseases of the genitourinary system. UrologySpermatozoa040201 dairy & animal scienceSpermBiomechanical PhenomenaPrincipal component analysisSperm MotilitySperm HeadAsian Journal of Andrology
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