Search results for "Amy"

showing 10 items of 1486 documents

Mutational analysis of 105 mucopolysaccharidosis type VI patients

2007

Mucopolysaccharidosis type VI (MPS VI; Maroteaux-Lamy syndrome) is a lysosomal storage disorder caused by mutations in the N-acetylgalactosamine-4-sulfatase (arylsulfatase B, ARSB) gene. ARSB is a lysosomal enzyme involved in the degradation of the glycosaminoglycans (GAG) dermatan and chondroitin sulfate. ARSB mutations reduce enzyme function and GAG degradation, causing lysosomal storage and urinary excretion of these partially degraded substrates. Disease onset and rate of progression is variable, producing a spectrum of clinical presentation. In this study, 105 MPS VI patients—representing about 10% of the world MPS VI population—were studied for molecular genetic and biochemical parame…

AdultArylsulfatase BAdolescentN-Acetylgalactosamine-4-SulfataseMPS VIDNA Mutational AnalysisNonsense mutationMucopolysaccharidosis type VIBiologyPolymorphism Single NucleotideGenetic HeterogeneityAge DistributionGene FrequencyGenotypeGeneticsmedicineHumansMissense mutationGenetic TestingChildCells CulturedGenetics (clinical)mucopolysaccharidosis type VIGlycosaminoglycansGeneticsMucopolysaccharidosis VIGenetic heterogeneityMucopolysaccharidosis VIMiddle Agedmedicine.diseasearylsulfatase BMaroteaux–Lamy syndromeDisease ProgressionARSBMaroteaux-LamyHuman Mutation
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Metabolic changes induced by combined prolonged exercise and low-calorie intake in man

1984

Thirteen middle-aged women and 10 men walked 344 km during 7 days. The daily walking distances were 57, 53, 67, 53, 41, 36, and 37 km at an average speed of 3.5 km X h-1. During the hike the subjects drank water, mineral drinks, and juices ad libitum. Except for some natural products, no food intake was allowed. During the hike the body weight and serum protein concentration of the subjects decreased by about 7%, on average. Serum triglyceride and total cholesterol decreased drastically, about 30-40% during the hike, but HDL-cholesterol showed a tendency to increase, giving a 40% increment in HDL/total cholesterol ratio. Serum free fatty acids rose 1.5-2 times above the starting level. Seru…

AdultBlood GlucoseMalemedicine.medical_specialtyEveningEpinephrinePhysiologymedicine.medical_treatmentPhysical ExertionPhysical exerciseFatty Acids NonesterifiedNorepinephrinechemistry.chemical_compoundPhysiology (medical)Internal medicinemedicineHumansInsulinTestosteroneOrthopedics and Sports MedicineAspartate AminotransferasesTriglyceridesTestosteroneTriglycerideCholesterolbusiness.industryInsulinBody WeightCholesterol HDLPublic Health Environmental and Occupational HealthFastinggamma-GlutamyltransferaseGeneral MedicineMetabolismMiddle AgedCholesterolEndocrinologychemistryFemaleEnergy IntakeEnergy MetabolismbusinessHormoneEuropean Journal of Applied Physiology and Occupational Physiology
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Transient and sustained BOLD signal time courses affect the detection of emotion-related brain activation in fMRI.

2014

A tremendous amount of effort has been dedicated to unravel the functional neuroanatomy of the processing and regulation of emotion, resulting in a well-described picture of limbic, para-limbic and prefrontal regions involved. Studies applying functional magnetic resonance imaging (fMRI) often use the block-wise presentation of stimuli with affective content, and conventionally model brain activation as a function of stimulus or task duration. However, there is increasing evidence that regional brain responses may not always translate to task duration and rather show stimulus onset-related transient time courses. We assume that brain regions showing transient responses cannot be detected in…

AdultBrain Mappingmedicine.diagnostic_testCognitive NeuroscienceRegulation of emotionEmotionsBrainCognitionStimulus (physiology)Affect (psychology)AmygdalaPeriaqueductal grayMagnetic Resonance Imagingmedicine.anatomical_structureNeurologymedicineImage Processing Computer-AssistedHumansFemaleTransient responsePsychologyFunctional magnetic resonance imagingNeuroscienceNeuroImage
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Influence of training and a maximal exercise test in analytical variability of muscular, hepatic, and cardiovascular biochemical variables.

2014

Short, middle, and long-term exercise, as well as the relative intensity of the physical effort, may influence a broad array of laboratory results, and it is thereby of pivotal importance to appropriately differentiate the 'physiologic' from the 'pathological' effects of exercise. Therefore, the values of some biomarkers in physically active subjects may be cautiously interpreted since the results may fall outside the conventional reference ranges. It has been demonstrated that middle and long-term endurance and/or strenuous exercise triggers transient elevations of muscular and cardiac biomarkers. However, no data have been published about the effect of short-term maximal exercise test on …

AdultCalcitoninMalemedicine.medical_specialtyCardiac biomarkersCardiovascular biomarkersCalcitonin Gene-Related PeptideClinical BiochemistryPhysical ExertionPhysical medicine and rehabilitationReference ValuesInternal medicineNatriuretic Peptide BrainmedicineCreatine Kinase MB FormHumansAspartate AminotransferasesProtein PrecursorsMuscle SkeletalPathologicalExerciseRelative intensitybiologyL-Lactate Dehydrogenasebusiness.industryC-reactive proteinSkeletal muscleHeartGeneral Medicinegamma-GlutamyltransferaseLaboratory resultsPeptide FragmentsTroponinmedicine.anatomical_structureexercise; laboratory; biomarkersC-Reactive ProteinLiverCardiologybiology.proteinExercise TestPhysical EnduranceMaximal exerciseSedentary BehaviorbusinesslaboratoryBiomarkersScandinavian journal of clinical and laboratory investigation
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The Resilient Emotional Brain: A Scoping Review of the Medial Prefrontal Cortex and Limbic Structure and Function in Resilient Adults With a History …

2020

Childhood Maltreatment (CM) is one of the strongest predictors of adult mental illness, though not all adults with CM develop psychopathology. Here, we describe the structure and function of emotional brain regions that may contribute to resilient functioning after CM. We review studies that report medial prefrontal cortex (mPFC), amygdala and hippocampus (‘limbic regions’) structure, function, and/or connections, in resilient (i.e., adults reporting CM without psychopathology) vs. vulnerable (i.e., adults reporting CM with psychopathology), or healthy adults (adults without CM with no psychopatology). We find that resilient adults have larger hippocampal grey and white matter volume, and i…

AdultCognitive Neurosciencemedia_common.quotation_subjectEmotionsPrefrontal CortexPoison controlBrain functionHippocampal formationAbuseAmygdala050105 experimental psychologyNeglectChildhood maltreatment03 medical and health sciences0302 clinical medicineNeurobiologyBrain structuremedicineHumans0501 psychology and cognitive sciencesRadiology Nuclear Medicine and imagingChild AbuseHabituationChildPrefrontal cortexNeglectBiological Psychiatrymedia_commonPsychopathologyResilience05 social sciencesBrainAmygdalaMental illnessmedicine.diseasemedicine.anatomical_structurenervous systemNeurology (clinical)Psychologypsychological phenomena and processes030217 neurology & neurosurgeryPsychopathologyClinical psychologyBiological Psychiatry: Cognitive Neuroscience and Neuroimaging
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Cells expressing markers of immature neurons in the amygdala of adult humans

2012

The polysialylated form of the neuronal cell adhesion molecule (PSA-NCAM) is expressed by immature neurons in the amygdala of adult mammals, including non-human primates. In a recent report we have also described the presence of PSA-NCAM-expressing cells in the amygdala of adult humans. Although many of these cells have been classified as mature interneurons, some of them lacked mature neuronal markers, suggesting the presence of immature neurons. We have studied, using immunohistochemistry, the existence and distribution of these immature neurons using post mortem material. We have also analysed the presence of proliferating cells and the association between immature neurons and specialise…

AdultDoublecortin Domain ProteinsMaleNeural Cell Adhesion Molecule L1AmygdalaWhite matterNeural Stem CellsAntigenParenchymamedicineAnimalsHumansSaimiriAgedNeuronsCATSbiologyGeneral NeuroscienceNeuropeptidesNeurogenesisMiddle AgedAmygdalaDoublecortinAdult Stem CellsKi-67 Antigenmedicine.anatomical_structurenervous systemAstrocytesCatsSialic Acidsbiology.proteinFemaleMicrotubule-Associated ProteinsNeuroscienceNeuronal Cell Adhesion MoleculeBiomarkersEuropean Journal of Neuroscience
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Carbohydrate-deficient transferrin (CDT) and HDL cholesterol (HDL) are highly correlated in male alcohol dependent patients.

2000

Background: Serum levels of total HDL cholesterol (HDL) are reportedly influenced by recent alcohol intake. We examined the correlation between HDL cholesterol and widely used markers of excessive alcohol intake, such as carbohydrate-deficient transferrin (CDT), γ-glutamyl-transferase (GGT), or mean corpuscular volume of erythrocytes (MCV), of which CDT is thought to be the most specific. Methods: Several serological markers [i.e., CDT, GGT, aspartate aminotransferase (ASAT), alanine aminotransferase (ALAT), MCV, and HDL] were determined in 100 actively drinking male patients with alcohol dependence (DSM-IV) and in 27 non-alcohol-dependent controls, according to routine procedures. Spearman…

AdultErythrocyte IndicesMalemedicine.medical_specialtyAdolescentCarbohydrate deficient transferrinMedicine (miscellaneous)AlcoholToxicologyStatistics Nonparametricchemistry.chemical_compoundInternal medicinemedicineHumansMean corpuscular volumeAgedchemistry.chemical_classificationEthanolmedicine.diagnostic_testbusiness.industryCholesterolAlcohol dependenceCholesterol HDLTransferringamma-GlutamyltransferaseMiddle AgedPsychiatry and Mental healthAlcoholismEndocrinologychemistryTransferrinToxicitylipids (amino acids peptides and proteins)businessBiomarkersAlcoholism, clinical and experimental research
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Vitamin B12 and hepatic enzyme serum levels correlate in male alcohol-dependent patients.

2001

- Vitamin B12 serum levels and markers for alcohol consumption were determined in 80 male alcohol-dependent patients. Spearman correlation coefficients (r(S)) were calculated. Significant positive correlations between vitamin B12 and hepatic enzyme values were found (gamma-glutamyltransferase: r(S) = 0.58; alanine aminotransferase: r(S) = 0.43; aspartate aminotransferase: r(S) = 0.47; glutamate dehydrogenase: r(S) = 0.43; all P:0.001). Therefore, for a proper interpretation of vitamin B12 levels, it may be clinically relevant to take markers of hepatocellular damage into account.

AdultErythrocyte IndicesMalemedicine.medical_specialtyCarbohydrate deficient transferrinAspartate transaminaseStatistics NonparametricGlutamate DehydrogenaseInternal medicineBlood plasmamedicineHumansCyanocobalaminVitamin B12Aspartate AminotransferasesLiver Diseases AlcoholicRetrospective StudiesbiologyGlutamate dehydrogenaseTransferrinnutritional and metabolic diseasesAlanine TransaminaseGeneral Medicinegamma-GlutamyltransferaseMiddle AgedAlcoholismVitamin B 12EndocrinologyAlanine transaminaseLiverToxicitybiology.proteinBiomarkersAlcohol and alcoholism (Oxford, Oxfordshire)
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Extraction of prefronto-amygdalar pathways by combining probability maps

2008

Many recent studies reported altered functional connectivity within the frontolimbic circuitry in a wide range of neuropsychiatric disorders. However, functional connectivity must rely on structural connections. In this study we applied a novel probabilistic fiber tracking method to assess the structural connectivity between the amygdala and different prefrontal brain regions in vivo. Twenty healthy subjects were investigated with diffusion tensor imaging. Probabilistic fiber tracking was started from the amygdala and different prefrontal brain regions. Resulting probability maps were combined using an extended multiplication of probabilistic maps to identify the most probable anatomical pa…

AdultExternal capsuleAdolescentNeuroscience (miscellaneous)Prefrontal CortexNerve Fibers MyelinatedAmygdalaBrain mappingYoung AdultNeural PathwaysBasal gangliamedicineHumansRadiology Nuclear Medicine and imagingPrefrontal cortexAnterior cingulate cortexProbabilityBrain MappingMiddle AgedAmygdalaDorsolateral prefrontal cortexPsychiatry and Mental healthDiffusion Magnetic Resonance Imagingmedicine.anatomical_structureFemaleNerve NetPsychologyNeuroscienceDiffusion MRIPsychiatry Research: Neuroimaging
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Cardiac MR enables diagnosis in 90% of patients with acute chest pain, elevated biomarkers and unobstructed coronary arteries

2015

To assess the diagnostic value of cardiac MRI (CMR) in patients with acute chest pain, elevated cardiac enzymes and a negative coronary angiogram.This study included a total of 125 patients treated in the chest pain unit during a 39-month period. Each included patient underwent MRI within a median of 3 days after cardiac catheterization. The MRI protocol comprised cine, oedema-sensitive and late gadolinium-enhancement imaging. The standard of reference was a consensus diagnosis based on clinical follow-up and the synopsis of all clinical, laboratory and imaging data.MRI revealed a multitude of diagnoses, including ischaemic cardiomyopathy (CM), dilated CM, myocarditis, Takotsubo CM, hyperte…

AdultGadolinium DTPAMalemedicine.medical_specialtyCardiac CatheterizationChest PainMyocarditismedicine.medical_treatmentContrast MediaMagnetic Resonance Imaging CineChest painCoronary AngiographyRisk AssessmentPredictive Value of TestsRisk FactorsInternal medicinemedicineHumansRadiology Nuclear Medicine and imagingMedical diagnosisCardiac catheterizationAgedAged 80 and overFull Paperbusiness.industryGeneral MedicineMiddle Agedmedicine.diseaseHypertensive heart diseaseCoronary arteriesmedicine.anatomical_structureCardiac amyloidosisCardiovascular DiseasesPredictive value of testscardiovascular systemCardiologyFemaleRadiologymedicine.symptombusinessBiomarkers
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