Search results for "Anomalías"

showing 10 items of 30 documents

Case report : partial uniparental disomy unmasks a novel recessive mutation in the LYST gene in a patient with a severe phenotype of Chediak-Higashi …

2021

Síndrome de Chédiak-Higashi; LYST; Disomia uniparental Síndrome de Chédiak-Higashi; LYST; Disomía uniparental Chédiak-Higashi syndrome; LYST; Uniparental disomy Chédiak-Higashi syndrome (CHS) is a rare autosomal recessive (AR) immune disorder that has usually been associated to missense, nonsense or indels mutations in the LYST gene. In this study, we describe for the first time the case of a CHS patient carrying a homozygous mutation in the LYST gene inherited as a result of a partial uniparental isodisomy (UPiD) of maternal origin. Sanger sequencing of the LYST cDNA and single nucleotide polymorphism (SNP)-arrays were performed to identify the causative mutation and to explain the molecul…

0301 basic medicineCHSLYSTCase ReportHemophagocytic lymphohistiocytosis030105 genetics & hereditymedicine.disease_causeLoss of heterozygosityExonCh&#233diak-Higashi syndromeImmunology and AllergyMissense mutation:Genetic Phenomena::Genetic Phenomena::Inheritance Patterns::Genes Recessive [PHENOMENA AND PROCESSES]Genetics:fenómenos genéticos::fenómenos genéticos::patrones de herencia::genes recesivos [FENÓMENOS Y PROCESOS]MutationPrimary immunodeficiencySistema inmune - Enfermedades - Diagnóstico.Loss of heterozygosityChédiak-Higashi Síndrome de - Diagnóstico.:enfermedades del sistema inmune::síndromes de inmunodeficiencia::disfunción bactericida del fagocito::síndrome de Chediak-Higashi [ENFERMEDADES]Uniparental disomyImmune system - Diseases - Diagnosis.Chromosome abnormalities.loss of heterozygositySNP array:fenómenos genéticos::variación genética::mutación::aberraciones cromosómicas::disomía uniparental [FENÓMENOS Y PROCESOS]lcsh:Immunologic diseases. AllergyAnomalías y malformaciones cromosómicas.disomia uniparentaluniparental disomy:Immune System Diseases::Immunologic Deficiency Syndromes::Phagocyte Bactericidal Dysfunction::Chediak-Higashi Syndrome [DISEASES]ImmunologyChédiak-Higashi syndromeSingle-nucleotide polymorphismBiologyprimary immunodeficiency03 medical and health sciencesMalalties immunològiquesmedicineGenetic disorders - Diagnosis.Béguez-Chédiak-Higashi syndrome - Diagnosis.Uniparental disomymedicine.diseaseSNP-array030104 developmental biologyAnomalies cromosòmiquesUniparental Isodisomyhemophagocytic lymphohistiocytosisEnfermedades genéticas - Diagnóstico.lcsh:RC581-607:Genetic Phenomena::Genetic Variation::Mutation::Chromosome Aberrations::Uniparental Disomy [PHENOMENA AND PROCESSES]
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International BEAT-PCD Consensus Statement for Infection Prevention and Control for Primary Ciliary Dyskinesia in collaboration with ERN-LUNG PCD Cor…

2021

Introduction In primary ciliary dyskinesia (PCD) impaired mucociliary clearance leads to recurrent airway infections and progressive lung destruction, and concern over chronic airway infection and patient-to-patient transmission is considerable. So far, there has been no defined consensus on how to control infection across centres caring for patients with PCD. Within the BEAT-PCD network, COST Action and ERS CRC together with the ERN-Lung PCD core a first initiative has now been taken towards creating such a consensus statement. Methods A multidisciplinary international PCD expert panel was set up to create a consensus statement for infection prevention and control (IP&C) for PCD, covering …

:Otros calificadores::Otros calificadores::/prevención & control [Otros calificadores]Infeccions respiratòries en els infantsPrimary Ciliary DyskinesiaStatement (logic)Respiratory SystemMULTICENTERRECOMMENDATIONS0302 clinical medicineOriginal Research ArticlesPandemicSTENOTROPHOMONAS-MALTOPHILIAInfection control:Pathological Conditions Signs and Symptoms::Pathologic Processes::Disease Attributes::Chronic Disease [DISEASES]030212 general & internal medicinePrimary ciliary dyskinesiaMalalties transmissibles - Transmissió:Environmental Health::Health::Environmental Illness::Communicable Diseases::Communicable Disease Control [PUBLIC HEALTH]FOUNDATIONbiologyTransmission (medicine)R:Congenital Hereditary and Neonatal Diseases and Abnormalities::Congenital Abnormalities::Abnormalities Multiple::Ciliopathies::Congenital Hereditary and Neonatal Diseases and Abnormalities::Ciliary Motility Disorders [DISEASES]:afecciones patológicas signos y síntomas::procesos patológicos::atributos de la enfermedad::enfermedad crónica [ENFERMEDADES]:salud ambiental::salud::enfermedad ambiental::enfermedades transmisibles::control de enfermedades transmisibles [SALUD PÚBLICA]medicine.anatomical_structureMedicinePatient representativesLife Sciences & BiomedicinePulmonary and Respiratory Medicinemedicine.medical_specialty3610 Medicine & health:enfermedades y anomalías neonatales congénitas y hereditarias::anomalías congénitas::anomalías múltiples::ciliopatías::enfermedades y anomalías neonatales congénitas y hereditarias::trastornos de la motilidad ciliar [ENFERMEDADES]:Other subheadings::Other subheadings::/prevention & control [Other subheadings]03 medical and health sciencesotorhinolaryngologic diseasesmedicineIntensive care medicineScience & TechnologyCYSTIC-FIBROSISLungbusiness.industryPSEUDOMONAS-AERUGINOSAMalalties cròniques - PrevencióCAREEFFICACYmedicine.diseasebiology.organism_classificationrespiratory tract diseases030228 respiratory systemNontuberculous mycobacteria610 Medizin und GesundheitbusinessERJ Open Research
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Role of cone-beam computed tomography (CBCT) in diagnosis and treatment planning of two-rooted maxillary lateral incisor with palatogingival groove. …

2020

Background: The embryonic root groove is an anatomical abnormality that starts in the cingulum and extends longitudinally down the long axis root towards the apex. This developmental anomaly is more frequently reported in maxillary lateral incisors. Gu YC in 2011 established three types of radicular grooves depending on its severity. According to this classification, type III presents a greater diagnostic and therapeutic complexity. The prevalence of palatogingival grooves in maxillary lateral incisors ranges from 1.9 to 14%. This case report provides valuable information about the diagnosis and treatment plan of palatogingival grooves with Cone-beam computed tomography (CBCT) scan. Case re…

Cone beam computed tomographyTomografíaIncisivoOdontologíaCase ReportPalpationOperative Dentistry and Endodontics03 medical and health sciences0302 clinical medicineMedicina preventivastomatognathic systemMedicinePeriodontal ProbingBone regenerationRadiation treatment planningTecnología médicaGeneral DentistryGroove (engineering)Cingulum (tooth)Maxillary lateral incisorOrthodonticsmedicine.diagnostic_testbusiness.industry030206 dentistry:CIENCIAS MÉDICAS [UNESCO]Anomalías dentariasstomatognathic diseasesUNESCO::CIENCIAS MÉDICASbusiness030217 neurology & neurosurgery
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La muntanya de L'Aixavegó: Un caso histórico de deslizamiento de grandes proporciones en la Ribera

1981

Deslizamientos de tierrasUNESCO::HISTORIAGeografíaUNESCO::HISTORIA::Historia por épocas::Historia antiguaMovimientos en masaClimasGeociencias. Medio ambienteLluvias torrenciales:HISTORIA::Historia por épocas::Historia antigua [UNESCO]ErosiónVertientes del taludAnomalías meteorológicasLitologíaGrupo BMorfología:HISTORIA [UNESCO]Taludes
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[Drugs use in pregnancy in the Valencia Region and the risk of congenital anomalies].

2017

Background Despite the potential risks of drug use during pregnancy, consumption has increased in recent decades. Objective To identify the risk of congenital anomalies (CA) associated with the use of drugs in primary care in pregnant women resident in the Valencia Region. Methods A case-control study, considering a case as a less than one year old live birth in 2009–2010, diagnosed with a CA and resident in the Valencia Region, obtained from the CA population-based registry. Controls were selected from the Metabolic Disease Registry, and the drugs prescribed and dispensed from the Integral Management of Pharmaceutical Services. Crude odds ratio (OR) was calculated with its 95% confidence i…

DrugAdultMalemedicine.medical_specialtyPreparación farmacéuticaEmbarazomedia_common.quotation_subjectPopulationLogistic regressionPediatricsRJ1-570Comunitat Valenciana03 medical and health sciencesYoung Adult0302 clinical medicinePregnancyRisk FactorsManagement of Technology and InnovationInternal medicineAmbulatory CareMedicineAnomalías congénitasHumans030212 general & internal medicineeducationmedia_commonPregnancyeducation.field_of_study030219 obstetrics & reproductive medicinebusiness.industryInfant NewbornAbnormalities Drug-InducedOdds ratioDexketoprofenmedicine.diseaseConfidence intervalSurgeryPregnancy ComplicationsSpainCase-Control StudiesFemalebusinessLive birthmedicine.drugFactores de riesgoAnales de pediatria (Barcelona, Spain : 2003)
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Oral manifestations in drug users : a review

2020

Background: In the dental environment there is not much talk about the oral manifestations resulting from the use of drugs, because in general the issue of drugs is a very difficult subject to deal with. Therefore, the objective of this work is to understand what are the most obvious manifestations in the oral cavity and as the dentist can detect them. Material and Methods: In order to carry out this bibliographical review, a scientific article search was made by consulting the PubMed database. The abstracts were read to recruit only what was consistent with the chosen topic. Results: The 23 sources of information affirmed the relationship between a bad state of general health, and more in …

Drugmedicine.medical_specialtyCaries dentalmedia_common.quotation_subjectOdontologíaReviewOral cavity03 medical and health sciences0302 clinical medicinemedicineMetanfetamina030212 general & internal medicineIntensive care medicineGeneral Dentistrymedia_commonPeriodontitisOral Medicine and PathologyMedicamento030505 public healthbusiness.industryAnomalías inducidas por medicamentosScientific articlemedicine.disease:CIENCIAS MÉDICAS [UNESCO]Meth mouthstomatognathic diseasesUNESCO::CIENCIAS MÉDICASGeneral health0305 other medical sciencebusiness
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Las lluvias torrenciales de septiembre de 1989 en el Mediterráneo español

1990

EL TRABAJO QUE ANALIZA LA VIOLENTA CICLOGENESIS QUE SE ABATIO SOBRE EL MEDITERRANEO ESPAÑOL EN SEPTIEMBRE DE 1989, INTENTA PONER DE MANIFIESTO LAS COMPLEJAS INTERACCIONES QUE ACTUAN PARA EL DESENCADENAMIENTO DE TALES FENOMENOS. SE INSISTE SOBRE TODO EN LA TRANSFERENCIA Y ACUMULACION DE ENERGIA TERMICA EN EL MAR COMO FACTOR DESTACADO DE ESTAS CICLOGENESIS. EL TRABAJO, TAMBIEN CON INQUIETUDES DIDACTICAS, MUESTRA COMO LA T.S.M. JUNTO CON OTROS PROCESOS GEOGRAFICOS, ATMOSFERICOS Y MEDIOAMBIENTALES, SON ELEMENTOS CRUCIALES PARA ENTENDER ESAS SEVERAS CICLOGENESIS. (A)

GeotermiaGeografíaUNESCO::HISTORIAAgua del marUNESCO::HISTORIA::Historia por épocas::Historia antiguaLluvias torrencialesGeociencias. Medio ambienteAnomalías térmicasFactores de influencia:HISTORIA::Historia por épocas::Historia antigua [UNESCO]Situaciones atmosféricasCiclogénesisGrupo B:HISTORIA [UNESCO]
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Effects of cardiopulmonary rehabilitation on the muscle function of children with Congenital Heart Disease : a prospective cohort study

2021

Critical medical and surgical advances have led to a shift in the care and management of children with congenital heart disease (CHD). These patients present with muscle deconditioning, which negatively influences their response to exercise, functional capacities, and quality of life. This study evaluates the influence of a cardiopulmonary rehabilitation program (CPRP) on the function of peripheral musculature of children with CHD. A single-center prospective cohort study was designed. Fifteen CHD subjects, between 12 and 16 years of age, with reduced aerobic capacity on a cardiopulmonary exercise test, were included in a three-month, 24-session CPRP. Measurements of the subjects’ handgrip …

Heart Defects CongenitalMúsculos - Fuerza - Entrenamiento.medicine.medical_specialtyEjercicio físico - Uso terapéutico.Heart diseaseHealth Toxicology and MutagenesisHeart - Abnormalities - Treatment.030204 cardiovascular system & hematologyBicepsArticle03 medical and health sciences0302 clinical medicineDeconditioningQuality of lifeMuscles - Training.Corazón - Anomalías y malformaciones - Tratamiento.HumansMedicineProspective Studies030212 general & internal medicineChildMuscle SkeletalProspective cohort studyEducación física para niños.Aerobic capacityChildren - Abnormalities - Treatment.congenital abnormalitiesHand Strengthexercisebusiness.industryCardiopulmonary rehabilitationRPublic Health Environmental and Occupational Healthmedicine.diseaseAdditional researchPhysical education and training for children.cardiac rehabilitationpediatricQuality of LifePhysical therapymuscle strengthMedicineAnomalías y malformaciones en los niños - Tratamiento.resistance trainingbusinessExercise - Therapeutic use.
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Changes in trunk posture and muscle responses in standing during pregnancy and postpartum

2018

Este artículo se encuentra disponible en la página web de la revista en la siguiente URL: https://journals.plos.org/plosone/article?id=10.1371/journal.pone.0194853 The aim of this study was to analyze the position of the lumbopelvic region and the muscle activation of erector spinae and biceps femoris muscles in a group of pregnant women in the third trimester. The hypothesis was that pregnancy-related biomechanical and morphological changes modify the position of the lumbopelvic region and the activation of extensor muscles. The position of the lumbar spine and pelvis in the sagittal plane, and the EMG activity of the erector spinae and biceps femoris muscles, were recorded during standing…

Maternal HealthPelvis - Muscles.lcsh:MedicineElectromyographyPathology and Laboratory MedicineBicepsBody Mass IndexBackache.0302 clinical medicineDolor pélvico.ElectricityPregnancyColumna vertebral - Propiedades mecánicas.Medicine and Health Scienceslcsh:ScienceMusculoskeletal Systemreproductive and urinary physiologyAbdominal MusclesLumbar VertebraeMultidisciplinarymedicine.diagnostic_testObstetricsMusclesPhysicsPostpartum PeriodObstetrics and GynecologyBioassays and Physiological Analysismedicine.anatomical_structurePelvis - Músculos.Physical SciencesFemaleAnatomyMuscle ElectrophysiologyResearch ArticleAdultmedicine.medical_specialtyPregnancy Trimester ThirdLower Back PainPosturePainLumbar vertebraeResearch and Analysis MethodsColumna vertebral - Músculos.PelvisPelvis - Mechanical properties.03 medical and health sciencesSigns and SymptomsDiagnostic MedicinePelvic pain.medicineHumansPelvis - Propiedades mecánicas.Lumbago.Spine - Muscles.Muscle SkeletalPelvisColumna vertebral - Anomalías y malformaciones.PregnancyDolor de espalda.HipElectromyographybusiness.industrylcsh:RElectrophysiological TechniquesBody WeightBiology and Life SciencesElectromagnetics030229 sport sciencesPregnant women.medicine.diseaseTrunkSpineBody HeightSagittal planeSpine - Abnormalities.Mujeres embarazadas.Women's HealthEmbarazo - Complicaciones y secuelas.lcsh:QbusinessPregnancy - Complications.Spine - Mechanical properties.030217 neurology & neurosurgeryPostpartum period
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Valor de los estudios cromosómicos en espermatozoides mediante la técnica de hibridación in situ fluorescente (FISH) en parejas estériles

2013

Los varones estériles presentan una frecuencia elevada de anomalías citogenéticas, algunas de ellas detectables mediante el cariotipo, pero otras limitadas a las células germinales como resultado de meiosis anormales. Con las nuevas técnicas de reproducción asistida como la Inyección Intracitoplásmica de Espermatozoides (ICSI), la fecundación por espermatozoides cromosómicamente anormales puede dar lugar a fallos de implantación, abortos de repetición y a la transmisión de anomalías cromosómicas a la descendencia. La hibridación in situ fluorescente (FISH) de espermatozoides es una técnica de análisis citogenético que, mediante el marcado de los cromosomas con moléculas de ADN fluorescentes…

PGDdiploidíaUNESCO::CIENCIAS MÉDICAS::Ciencias clínicas::Genética clínicaUNESCO::CIENCIAS DE LA VIDA::Biología humana::Genética humanaICSIFIVembrionesEspermatozoidesFISHaneuploidíaanomalías cromosómicas:CIENCIAS DE LA VIDA::Biología humana::Genética humana [UNESCO]:CIENCIAS MÉDICAS::Ciencias clínicas::Genética clínica [UNESCO]
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