Search results for "Lep"

showing 10 items of 3622 documents

Enhanced tonic GABAA inhibition in typical absence epilepsy

2009

The cellular mechanisms underlying typical absence seizures, which characterize various idiopathic generalized epilepsies, are not fully understood, but impaired γ-aminobutyric acid (GABA)-ergic inhibition remains an attractive hypothesis. In contrast, we show here that extrasynaptic GABAA receptor–dependent 'tonic' inhibition is increased in thalamocortical neurons from diverse genetic and pharmacological models of absence seizures. Increased tonic inhibition is due to compromised GABA uptake by the GABA transporter GAT-1 in the genetic models tested, and GAT-1 is crucial in governing seizure genesis. Extrasynaptic GABAA receptors are a requirement for seizures in two of the best character…

GABA Plasma Membrane Transport ProteinsGABA Plasma Membrane Transport ProteinsCellular pathologystargazerBiologyPharmacologytonic currentSettore BIO/09 - FisiologiaArticleGeneral Biochemistry Genetics and Molecular BiologyTonic (physiology)spike–and–wave discharge03 medical and health sciencesEpilepsy0302 clinical medicineThalamusthalamusGenetic modelmedicineAnimalsGABA transporterGABA-A Receptor AntagonistsReceptorTHIP030304 developmental biology0303 health sciencesextrasynaptic tonic current GAT–1 thalamus spike–and–wave discharge GAERS stargazer lethargic GHB THIPGABAA receptorAminobutyratesPetit mal epilepsyGeneral Medicineextrasynapticmedicine.diseaseReceptors GABA-ARats3. Good healthEpilepsy Absenceabsence epilepsy GABA electrophysiology patch clampnervous systemGAT–1GAERSbiology.proteinlethargicGHB030217 neurology & neurosurgery
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The inhibitory neural circuitry as target of antiepileptic drugs.

2001

Impairments and defects in the inhibitory neurotransmission in the CNS can contribute to various seizure disorders, i.e., gamma-aminobutyric acid (GABA) and glycine as the main inhibitory neurotransmitters in the brain play a crucial role in some forms of epilepsy. Recent advances in deciphering the molecular basis of the GABAergic and glycinergic systems has been achieved by means of cloning techniques and gene targeting strategies in animals, contributing to the understanding of drug action. As well, several anticonvulsive substances emerged which target key molecules of the inhibitory systems. Employment of recombinant expression systems, including, but not restricted to the inhibitory c…

GABA Plasma Membrane Transport ProteinsGABA Plasma Membrane Transport ProteinsOrganic Anion TransportersDrug actionPharmacologyNeurotransmissionBiologyInhibitory postsynaptic potentialBiochemistrySynaptic TransmissionGABA AntagonistsEpilepsyDrug DiscoverymedicineAnimalsHumansGlycine receptorgamma-Aminobutyric AcidPharmacologyEpilepsyOrganic ChemistryMembrane ProteinsMembrane Transport Proteinsmedicine.diseaseReceptors GABA-AMechanism of actionReceptors GABA-BMolecular MedicineGABAergicAnticonvulsantsmedicine.symptomCarrier ProteinsCurrent medicinal chemistry
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Lack of SCN1A Mutations in Familial Febrile Seizures

2002

Summary:  Purpose: Mutations in the voltage-gated sodium channel subunit gene SCN1A have been associated with febrile seizures (FSs) in autosomal dominant generalized epilepsy with febrile seizures plus (GEFS+) families and severe myoclonic epilepsy of infancy. The present study assessed the role of SCN1A in familial typical FSs. Methods: FS families were selected throughout a collaborative study of the Italian League Against Epilepsy. For each index case, the entire coding region of SCN1A was screened by denaturant high-performance liquid chromatography. DNA fragments showing variant chromatograms were subsequently sequenced. Results: Thirty-two FS families accounting for 91 affected indiv…

GAMMA-2-SUBUNITMaleFebrile convulsionsDNA Mutational Analysismedicine.disease_causePolymerase Chain ReactionSodium ChannelsFebrileEpilepsyExonPLUSDNA Mutational AnalysisGene duplicationChildIndex caseChromatography High Pressure LiquidGeneticsChromatographyMutationIdiopathic epilepsyExonsNeurologyIon channelsHigh Pressure LiquidFemaleGeneralized epilepsy with febrile seizures plusMutationsAdultAdolescentGENERALIZED EPILEPSYNerve Tissue ProteinsSeizures FebrileSeizuresGeneticsmedicineHumansFamilybusiness.industryCONVULSIONSGene AmplificationSODIUM-CHANNELmedicine.diseaseGENEDYSFUNCTIONNAV1.1 Voltage-Gated Sodium ChannelFebrile convulsions; Genetics; Idiopathic epilepsy; Ion channels; Mutations; Adolescent; Adult; Child; Chromatography High Pressure Liquid; DNA Mutational Analysis; Exons; Female; Gene Amplification; Humans; Male; Mutation; NAV1.1 Voltage-Gated Sodium Channel; Nerve Tissue Proteins; Polymerase Chain Reaction; Seizures Febrile; Sodium Channels; FamilyMutationMyoclonic epilepsyNeurology (clinical)businessEpilepsia
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Alteraciones en la homeostasis del transportador de glutamato GLT-1 en la Enfermedad de Lafora

2017

Tesis doctoral, 192 páginas, figuras y tablas

GLT-1transporte glutamatoGlutamatoUbicuitinaciónglutamatoubicuitinaciónendocitosisTransporte glutamatoLaforaEAAAT2EndocitosisepilepsiaEpilepsia
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Study of elementary reactions with the hades dielectron spectrometer

2010

Results obtained with the HADES dielectron spectrometer at GSI are discussed, with emphasis on dilepton production in elementary reactions. Díaz Medina, José, Jose.Diaz@uv.es ; Gil Ortiz, Alejandro, Alejandro.Gil@ific.uv.es

GSIHADES Dielectron Spectometer ; GSI ; Dilepton Production ; Elementary ReactionsElementary Reactions:FÍSICA [UNESCO]HADES Dielectron SpectometerUNESCO::FÍSICADilepton ProductionUNESCO::FÍSICA::Física molecular::Moléculas mesónicas y muónicas:FÍSICA::Física molecular::Moléculas mesónicas y muónicas [UNESCO]
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New records of gall-inducer and inquiline insects in a few mediterranean countries, with biological notes

2014

An annotated list of some gall-inducing and inquiline insects found on herbaceous plants and trees in Italy and in other few Mediterranean countries is reported. Among the gall-inducer species, Phanacis phoenixopodos (Mayr, 1882) is new for the Italian peninsula, Callirhytis rufescens (Mayr, 1882), Andricus quercusramuli (L., 1761) and Plagiotrochus amenti Kieffer, 1901 (Cynipidae: Hymenoptera) are new for Sicily; the latter was previously cited from Italy without collecting data. Oecocecis guyonella Guenée, 1870 was found in Libya and Amblypalpis olivierella Ragonot, 1886 (Gelechiidae: Lepidoptera) in Jordan, Libya, Northern Yemen, and the United Arab Emirates. In addition, Saphonecrus gal…

Gall-inducing insects Hymenoptera Cynipidae Lepidoptera Gelechiidae biological cycleSettore AGR/11 - Entomologia Generale E Applicata
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Teleportation of squeezing: optimization using non-Gaussian resources

2010

We study the continuous-variable quantum teleportation of states, statistical moments of observables, and scale parameters such as squeezing. We investigate the problem both in ideal and imperfect Vaidman-Braunstein-Kimble protocol setups. We show how the teleportation fidelity is maximized and the difference between output and input variances is minimized by using suitably optimized entangled resources. Specifically, we consider the teleportation of coherent squeezed states, exploiting squeezed Bell states as entangled resources. This class of non-Gaussian states includes photon-added and photon-subtracted squeezed states as special cases. At variance with the case of entangled Gaussian re…

GaussianFOS: Physical sciencesQuantum entanglement01 natural sciencesTeleportation010305 fluids & plasmassymbols.namesakeQuantum mechanics0103 physical sciencesStatistical physics010306 general physicsQuantum information sciencePhysicsQuantum PhysicsBell stateCavity quantum electrodynamicsObservableQuantum PhysicsAtomic and Molecular Physics and OpticsCondensed Matter - Other Condensed MattersymbolsQuantum Physics (quant-ph)Quantum teleportationPhysics - OpticsOther Condensed Matter (cond-mat.other)Optics (physics.optics)
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Tunable non-Gaussian resources for continuous-variable quantum technologies

2013

We introduce and discuss a set of tunable two-mode states of continuous-variable systems, as well as an efficient scheme for their experimental generation. This novel class of tunable entangled resources is defined by a general ansatz depending on two experimentally adjustable parameters. It is very ample and flexible as it encompasses Gaussian as well as non-Gaussian states. The latter include, among others, known states such as squeezed number states and de-Gaussified photon-added and photon-subtracted squeezed states, the latter being the most efficient non-Gaussian resources currently available in the laboratory. Moreover, it contains the classes of squeezed Bell states and even more ge…

GaussianFOS: Physical sciencesTopology01 natural sciencesTeleportation010309 opticssymbols.namesakeQuantum mechanics0103 physical sciencesQuantum information010306 general physicsPhysicsBell stateQuantum PhysicsQuantum PhysicsAtomic and Molecular Physics and OpticsQuantum technologyCondensed Matter - Other Condensed MattersymbolsCoherent statesQuantum Physics (quant-ph)Realization (systems)Quantum teleportationOther Condensed Matter (cond-mat.other)Optics (physics.optics)Physics - Optics
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Analysis of myxoma virus genome using pulsed-field gel electrophoresis

1996

A method is presented for the isolation of large quantities of myxoma virus DNA using pulsed-field gel electrophoresis (PFGE), and some preliminary applications of this technique.

Gel electrophoresisGeneral Veterinarybiology[SDV]Life Sciences [q-bio]Myxoma virusMyxoma virusGenome ViralPoxviridae InfectionsGeneral Medicinebiology.organism_classificationMicrobiologyGenomeDNA extractionVirologyMolecular biologyVirusElectrophoresis Gel Pulsed-Field[SDV] Life Sciences [q-bio]DNA Viralcardiovascular systemPulsed-field gel electrophoresisAnimalsPoxviridaeRabbitsLeporipoxvirus
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Horizontally transmitted parasitoid killing factor shapes insect defense to parasitoids

2021

Protection from parasitism by a virus Parasitoid wasps have developed myriad systems to overcome the defense mechanisms of their hosts as they lay their eggs in the bodies and eggs of targeted species. Gasmi et al . report how the host can fight back when infected by a virus that expresses a protein conferring resistance to the parasitoid. When members of the butterfly and moth family are targeted by wasps, a protein family has evolved that is horizontally carried by viruses—and sometimes is incorporated into the host genome—and impairs the ability of parasitoid offspring to fully develop and emerge. Characterizing the ability of this protein to protect hosts against specific parasites, the…

Gene Transfer Horizontalmedia_common.quotation_subjectGenome InsectWaspsZoologyParasitismApoptosisInsect VirusesInsectSpodopteraCompetition (biology)Host-Parasite InteractionsParasitoidLepidoptera genitaliaViral Proteins03 medical and health sciences0302 clinical medicineEvolutionary arms raceAnimals030304 developmental biologymedia_common0303 health sciencesMultidisciplinarybiologyHost (biology)fungibiology.organism_classificationBiological EvolutionMicrogastrinaeNucleopolyhedrovirusesLepidopteraLarvaEntomopoxvirinaeInsect Proteins030217 neurology & neurosurgeryScience
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