Search results for "Malin"

showing 10 items of 110 documents

Genotype-phenotype correlations in nemaline myopathy caused by mutations in the genes for nebulin and skeletal muscle alpha-actin.

2003

We present comparisons of the clinical pictures in a series of 60 patients with nemaline myopathy in whom mutations had been identified in the genes for nebulin or skeletal muscle alpha-actin. In the patients with nebulin mutations, the typical form of nemaline myopathy predominated, while severe, mild or intermediate forms were less frequent. Autosomal recessive inheritance had been verified or appeared likely in all nebulin cases. In the patients with actin mutations, the severe form of nemaline myopathy was the most common, but some had the mild or typical form, and a few showed other associated features such as intranuclear rods or actin accumulation. Most cases were sporadic, but in ad…

AdultMalePathologymedicine.medical_specialtyAdolescentGenotypeNonsense mutationDNA Mutational AnalysisMuscle ProteinsBiologymedicine.disease_causeMyopathies Nemaline03 medical and health sciencesNebulin0302 clinical medicineNemaline myopathyGenotypemedicineHumansChildMuscle SkeletalGenetics (clinical)Actin030304 developmental biologyGenetics0303 health sciencesMutationInfantmedicine.diseaseCongenital myopathyPhenotypeActinsPhenotypeNeurologyChild PreschoolPediatrics Perinatology and Child HealthMutationbiology.proteinFemaleNeurology (clinical)030217 neurology & neurosurgeryNeuromuscular disorders : NMD
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Lichen rehydration in heavy metal polluted environments: Pb modulates the oxidative response of both Ramalina farinacea thalli and its isolated micro…

2014

Lichens are adapted to desiccation/rehydration and accumulate heavy metals, which induce ROS especially from the photobiont photosynthetic pigments. Although their mechanisms of abiotic stress tolerance are still to be unravelled, they seem related to symbionts' reciprocal upregulation of antioxidant systems. With the aim to study the effect of Pb on oxidative status during rehydration, the kinetics of intracellular ROS, lipid peroxidation and chlorophyll autofluorescence of whole Ramalina farinacea thalli and its isolated microalgae (Trebouxia TR1 and T. TR9) was recorded. A genetic characterization of the microalgae present in the thalli used was also carried out in order to assess possib…

ChlorophyllTrebouxiaLichensSoil ScienceBiologyPhotosynthesisRamalina farinaceaLipid peroxidationchemistry.chemical_compoundAscomycotaChlorophytaBotanyFluorometrySymbiosisEcology Evolution Behavior and SystematicsEcologyAbiotic stressWaterbiology.organism_classificationThallusLeadchemistrySpainChlorophyllBotànicaEnvironmental PollutantsLipid PeroxidationReactive Oxygen SpeciesDesiccation
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Commenti a “Bronislaw Malinowski, l’antropologia pratica, la politica e il colonialismo” di Antonino Colajanni, con una risposta dell’autore

2022

Commenti a “Bronislaw Malinowski, l’antropologia pratica, la politica e il colonialismo” di Antonino Colajanni, con contributi di Marco Bassi, Valeria Ribeiro Corossacz, Antonio De Lauri, Frederico Delgado Rosa, Andrea E. Pia, Leonardo Piasere, Daniela Salvucci, Ivan Severi, Barbara Sorgoni, Jaro Stacul, Giuseppe Tateo, Elisabeth Tauber, Dorothy L. Zinn, Pier Paolo Viazzo e una risposta dell’autore.

Malinowski antropologia applicata antropologia pratica colonialismoMalinowskicolonialismoAntropologia applicataSettore M-DEA/01 - Discipline Demoetnoantropologicheantropologia pratica
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Neonatal form of nemaline myopathy, muscle immaturity, and a microvascular injury.

1990

An infant with a neonatal form of nemaline myopathy showed ultrastructural features of muscle immaturity. Immaturity was characterized by an abnormal presence of myotubes, as well as cells in clusters within a common basement membrane and a great number of satellite cells adhering to very small muscle fibers. In addition, degenerative changes and a severe microvascular lesion were observed. The pathologic findings in the muscle of this patient were those of neonatal nemaline myopathy complicating severe microvascular injury, possibly induced by an unknown toxic agent. ( J Child Neurol 1990;5:122-126).

Pathologymedicine.medical_specialtyMuscle HypotoniaBiopsyIschemiaBiologyMuscle Smooth VascularLesion03 medical and health sciences0302 clinical medicineNemaline myopathyMyofibrilsIschemia030225 pediatricsBiopsymedicineHumansBasement membraneInclusion BodiesAsphyxia NeonatorumRespiratory Distress Syndrome Newbornmedicine.diagnostic_testMyogenesisMicrocirculationMusclesInfant NewbornDisseminated Intravascular Coagulationmedicine.diseaseMicroscopy ElectronMuscular Atrophymedicine.anatomical_structurePediatrics Perinatology and Child HealthMuscle HypotoniaFemaleNeurology (clinical)medicine.symptomMyofibril030217 neurology & neurosurgeryJournal of child neurology
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Negoziazioni: aspetti metodologici e territori di confine nel racconto di vita di Gaspare Spatuzza

2017

Il paper approfondisce alcune questioni metodologiche emerse nel corso di un progetto di ricerca iniziato nell’ottobre del 2012, quando – ottenute le formali autorizzazioni – ho intervistato per la prima volta Gaspare Spatuzza. Gli incontri – 9 in tutto e dispiegatisi lungo l’arco di un anno fino all’ottobre del 2013 – si sono svolti all’interno della struttura carceraria in località protetta dove Spatuzza si trovava detenuto. La ricerca si è conclusa con la pubblicazione di un volume dal titolo A colloquio con Gaspare Spatuzza. Un racconto di vita. Una storia di stragi (Bologna, il Mulino, 2016). I temi oggetto di approfondimento di questo lavoro sono stati al centro dei miei interessi di …

Settore SPS/08 - Sociologia Dei Processi Culturali E ComunicativiSettore SPS/12 - Sociologia Giuridica Della Devianza E Mutamento Socialerécit de vie raconto autobiografico Gaspare Spatuzza stragi trattativa ambiguità malinteso
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A comparative study of the effect of UV and formalin inactivation on the stability and immunogenicity of a Coxsackievirus B1 vaccine

2019

Type B Coxsackieviruses (CVBs) belong to the enterovirus genus, and they cause both acute and chronic diseases in humans. CVB infections usually lead to flu-like symptoms but can also result in more serious diseases such as myocarditis, aseptic meningitis and life-threatening multi-organ infections in young infants. Thus, CVBs have long been considered as important targets of future vaccines. We have previously observed CVB1 capsid disintegration and virus concentration decrease with 12-day long formalin inactivation protocol. Here a scalable ion exchange chromatography purification method was developed, and purified CVB1 was inactivated with UV-C or formalin. Virus morphology and concentra…

enteroviruksetcoxsackievirus BBiolääketieteet - Biomedicinerokotteetultraviolettisäteilyinactivated vaccineformaldehydiformalinUV
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A new method to isolate lichen algae by using percoll® gradient centrifugation

2001

AbstractA rapid method to isolate intact functional algae from the lichens Evemia prunastri and Ramalina farinacea has been developed. This method is based on the use of Percoll® gradients after mechanical disruption of lichen thalli. Results obtained show that the algal preparations were virtually free of contamination by fungal hyphae. The purified algal cells were photosynthetically active and without symptoms of photoinhibition, which indicates their functional integrity. This method may be used for the isolation of intact algae from a broad range of lichen species.

Algal cellsPhotoinhibitionAlgaebiologyEvernia prunastriBotanyPercoll gradient centrifugationLichenbiology.organism_classificationEcology Evolution Behavior and SystematicsRamalina farinaceaThallusThe Lichenologist
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Histophotometry: a new method for automated histological examination of solid tissue samples demonstrated on bladder cancer.

1979

The purpose of this study was to demonstrate the ability of a new method to discriminate between benign and malignant tissue. Tissue samples from three patients with bladder tumours and one patient with bladder diverticula have been examined by histophotometry. This method, based on the correlation of nuclear volume and nucleic acid contents per cell uses thick formalin fixed samples. The results are obtained by measurements averaging more than one hundred thousand cells per sample. By this histophotometric examination a clear differentiation between malignant and benign tissue could be achieved. It was also possible to determine the degree of malignancy and to differentiate between infiltr…

Thousand cellsPathologymedicine.medical_specialtyBladder cancerUrologyHistological TechniquesHistologyFormalin fixedBiologyIn Vitro TechniquesMalignancymedicine.diseaseSolid tissuePhotometryBladder TissueUrinary Bladder NeoplasmsmedicineHumansHistological examinationUrological research
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Malinowski and Bloch in the Field: Fragments, Beginnings and Imaginations

2010

Lo zoccolo molle e più clandestino del saggio è costituito dallo smussamento graduale, ma incondizionato della nozione di autore in favore di una funzione autore che consente di meglio fare emergere (o, viceversa, fare sparire), sull’esempio di Foucault, la consistenza apparente di un atto originario dietro il brusio delle voci della cultura. Il contributo è più apertamente incentrato sulla comparazione inedita di un antropologo e di uno storico: Bronislaw Malinowski e Marc Bloch. Mi sono servito intenzionalmente della ‘comparazione’ allo scopo di tentare un montaggio di alcuni testi dei due autori (alieni l’uno all’altro per formazione e per esperienze teoriche) e il mio stesso, graduale e…

Malinowski Bloch Storie di vitaimmaginazione nozione di inizioSettore M-DEA/01 - Discipline Demoetnoantropologiche
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The Ti-influence on the tourmaline color

2008

Titanium was examined in different black tourmalines by spectrophotometric analyses in the region between 12500 and 27000 cm-1 (800-370 nm) using a microscope spectrophotometer MPV-5P, Leitz (Germany), and chemically analyzed on an electron microprobe Camebax Microbeam, Cameca (France) in WDS Mode. Fourteen tourmaline samples with their face oriented parallel to the principal axis, cut and polished down to thin sections, showed polarized spectra of two broad absorption bands at approximately 14000 cm-1 (715 nm) and 24000 cm-1 (417 nm). Precision thickness measurements were used to calculate the absorption coefficients α. For the absorption around 24000 cm-1, a linear correlation was observe…

tourmalineMicroscopeTourmalineChemistryAnalytical chemistrychemistry.chemical_elementGeneral ChemistryElectron microprobeMicrobeamIntervalence charge transferSpectral linelaw.inventionlawIVCT effecttitaniumAbsorption (electromagnetic radiation)Titanium
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