Search results for "Stein-"

showing 10 items of 77 documents

Expanding the phenotype associated to KMT2A variants: overlapping clinical signs between Wiedemann–Steiner and Rubinstein–Taybi syndromes

2020

Lysine-specific methyltransferase 2A (KMT2A) is responsible for methylation of histone H3 (K4H3me) and contributes to chromatin remodeling, acting as “writer” of the epigenetic machinery. Mutations in KMT2A were first reported in Wiedemann–Steiner syndrome (WDSTS). More recently, KMT2A variants have been described in probands with a specific clinical diagnosis comprised in the so-called chromatinopathies. Such conditions, including WDSTS, are a group of overlapping disorders caused by mutations in genes coding for the epigenetic machinery. Among them, Rubinstein–Taybi syndrome (RSTS) is mainly caused by heterozygous pathogenic variants in CREBBP or EP300. In this work, we used next generati…

AdultMaleRubinstein-Taybi SyndromeAdolescentHistone-Lysine N-MethyltransferaseWiedemann–SteinerArticlePhenotypeSettore MED/03 - Genetica MedicaSettore MED/38 - PEDIATRIA GENERALE E SPECIALISTICAKMT2A variantsMutationHumansFemaleEpigeneticsRubinstein–Taybi syndromesChildKMT2A Gene Wiedemann–Steiner syndrome Rubinstein–Taybi syndromeMyeloid-Lymphoid Leukemia Protein
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Prevalence of herpes simplex, Epstein Barr and human papilloma viruses in oral lichen planus.

2011

Objectives: The aim of the present study was to assess the prevalence of Herpes Simplex virus, Epstein Barr virus and Human Papilloma virus -16 in oral lichen planus cases and to evaluate whether any clinical variant, histopathological or demographic feature correlates with these viruses. Study Design: The study was conducted on 65 cases. Viruses were detected immunohistochemically. We evaluated the histopathological and demographic features and statistically analysed correlation of these features with Herpes Simplex virus, Epstein Barr virus and Human Papilloma virus-16 positivity. Results: Herpes Simplex virus was positive in six (9%) cases and this was not statistically significant. The …

AdultMaleSimplexvirusHerpesvirus 4 Humanfood.ingredientvirusesmedicine.disease_causeVirusYoung Adultfoodstomatognathic systemmedicineHumansSimplexvirusskin and connective tissue diseasesGeneral DentistryPathologicalAgedHuman papillomavirus 16integumentary systembusiness.industryEpstein-Barr Virus PositiveMiddle Agedmedicine.disease:CIENCIAS MÉDICAS [UNESCO]Epstein–Barr virusVirologystomatognathic diseasesHerpes simplex virusCross-Sectional StudiesOtorhinolaryngologyImmunologyUNESCO::CIENCIAS MÉDICASPapillomaSurgeryOral lichen planusFemalebusinessLichen Planus OralMedicina oral, patologia oral y cirugia bucal
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Clinicopathological characteristics of Epstein-Barr virus-positive gastric cancer in Latvia

2019

Objective Epstein-Barr virus (EBV)-associated gastric cancer has been proposed to be a distinct gastric cancer molecular subtype. The prognostic significance of EBV infection in gastric cancer remains unclear and needs further investigation. Our study aimed to analyze EBV-positive and EBV-negative gastric cancer patients regarding their personal and tumor-related characteristics, and compare their overall survival. Methods Gastric cancer patients consecutively treated at the Riga East University Hospital during 2009-2016 were identified retrospectively. Tumor EBV status was determined by in-situ hybridization for EBV-encoded RNA (EBER). Information about clinicopathological characteristics …

AdultMalemedicine.medical_specialtyEpstein-Barr Virus InfectionsComorbidityKaplan-Meier EstimateAdenocarcinomaGastroenterologyHospital recordsArticle03 medical and health sciencesYoung Adult0302 clinical medicineAge DistributionStomach NeoplasmsInternal medicinehemic and lymphatic diseasesmedicineHumansStage (cooking)Sex DistributionAgedNeoplasm StagingProportional Hazards ModelsRetrospective StudiesAged 80 and overHepatologyStage I Gastric Cancerbusiness.industryHazard ratioSmokingGastroenterologyCancerEpstein-Barr Virus PositiveMiddle AgedOverweightUniversity hospitalmedicine.diseasePrognosisLatviaConfidence intervalSurvival Rate030220 oncology & carcinogenesis030211 gastroenterology & hepatologyFemaleNeoplasm Gradingbusiness
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Acute acalculous cholecystitis during the course of primary Epstein–Barr virus infection: a new case and a review of the literature

2008

Summary Objective The aim of this study was to describe a case of acute acalculous cholecystitis occurring in the course of primary Epstein–Barr virus (EBV) infection. Methods The clinical features of the case were analyzed and compared to those of three other similar cases reported in the international literature. Results All cases occurred in European females with cholestatic hepatitis, presented with gallbladder wall thickening, and recovered uneventfully without the need for surgical intervention. Conclusions Acute acalculous cholecystitis may occur during the course of acute EBV infection, especially in patients with cholestatic hepatitis. Clinicians should be aware of the possible inv…

AdultMicrobiology (medical)Epstein-Barr Virus Infectionsmedicine.medical_specialtyAdolescentmedicine.disease_causeGastroenterologyHerpesviridaeVirusacute acalculous; chotecystitis; gallbladder; Epstein-Barr virus; infectious mononucleosisEpstein–Barr virusInternal medicinemedicineEpstein-Barr viruschotecystitiHumansGammaherpesvirinaeInfectious mononucleosisEpstein–Barr virus infectionAcalculous Cholecystitischotecystitisbiologybusiness.industryGallbladderAcute acalculous cholecystitisGallbladderacute acalculousEpstein-Barr viruGeneral MedicineMiddle Agedbiology.organism_classificationmedicine.diseaseEpstein–Barr virusmedicine.anatomical_structureInfectious DiseasesImmunologyCholecystitisacute acalculouFemaleViral diseasebusinessInternational Journal of Infectious Diseases
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Depletion of alloreactive T cells via CD69: implications on antiviral, antileukemic and immunoregulatory T lymphocytes

2005

Selective depletion of alloreactive T cells from stem-cell allografts should abrogate graft-versus-host disease while preserving beneficial T cell specificities to facilitate engraftment and immune reconstitution. We therefore explored a refined immunomagnetic separation strategy to effectively deplete alloreactive donor lymphocytes expressing the activation antigen CD69 upon stimulation, and examined the retainment of antiviral, antileukemic, and immunoregulatory T cells. In addition to the CD69high T cell fraction, our studies retrieved two T cell subsets based on residual CD69 expression. Whereas, truly CD69(neg) cells were devoid of detectable alloresponses to original stimulators, CD69…

Antigens Differentiation T-LymphocyteCD4-Positive T-LymphocytesEpstein-Barr Virus InfectionsHerpesvirus 4 HumanT cellCytomegalovirusGraft vs Host DiseaseCell Cycle Proteinschemical and pharmacologic phenomenaStreptamerBiologyLymphocyte ActivationLymphocyte DepletionCell LineInterleukin 21Antigens CDmedicineHumansTransplantation HomologousCytotoxic T cellLectins C-TypeIL-2 receptorAntigen-presenting cellTransplantationHematopoietic Stem Cell TransplantationNuclear ProteinsForkhead Transcription FactorsReceptors Interleukin-2hemic and immune systemsHematologyT lymphocyteNatural killer T cellDNA-Binding Proteinsmedicine.anatomical_structureCytomegalovirus InfectionsImmunologyRNA Splicing FactorsCarrier ProteinsImmunologic MemoryBone Marrow Transplantation
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Itô calculus extended to systems driven by -stable Lévy white noises (a novel clip on the tails of Lévy motion)

2007

Abstract The paper deals with probabilistic characterization of the response of non-linear systems under α -stable Levy white noise input. It is shown that, by properly selecting a clip in the probability density function of the input, the moments of the increments of Levy motion process remain all of the same order ( d t ) , like the increments of the Compound Poisson process. It follows that the Ito calculus extended to Poissonian input, may also be used for α -stable Levy white noise input processes. It is also shown that, when the clip on the tails of the probability of the increments of the Levy motion approaches to infinity, the Einstein–Smoluchowsky equation is restored. Once these c…

Applied MathematicsMechanical Engineeringmedia_common.quotation_subjectMonte Carlo methodMathematical analysisTruncated Lévy motionProbabilistic logicProbability density functionItô calculuWhite noiseExtension (predicate logic)InfinityLévy processMechanics of Materialsα-Stable processeCompound Poisson processEinstein-Smoluchowsky equationMathematicsmedia_commonInternational Journal of Non-Linear Mechanics
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Angioimmunoblastic T-cell lymphoma

2008

Angioimmunoblastic T-cell lymphoma (AITL) is a rare and aggressive neoplasm clinically characterized by sudden onset of constitutional symptoms, lymphadenopathy, hepatosplenomegaly, frequent autoimmune phenomena, particularly hemolytic anemia and thrombocytopenia, and polyclonal hypergammaglobulinemia. The lymph node histological picture is also distinctive, constituted by a polymorphic infiltrate, a marked proliferation of high endothelial venules, and a dense meshwork of dentritic cells. The neoplastic CD4+ T-cells represent a minority of the lymph node cell population; its detection is facilitated by the aberrant expression of CD10. Almost all cases arbor an EBV infected B-cell populatio…

CD4-Positive T-LymphocytesMaleEpstein-Barr Virus InfectionsPathologyAutologous transplantHerpesvirus 4 HumanHepatosplenomegalyImmunosuppressive AgentEpstein-Barr Virus InfectionHypergammaglobulinemiaLymph nodeNon-Hodgkin lymphomaAngioimmunoblastic lymphomaB-Lymphocyteseducation.field_of_studyB-LymphocyteLymph NodeHematologyThalidomideSurvival RateTransplantation Autologoumedicine.anatomical_structureOncologyCD4-Positive T-LymphocyteFemaleNeprilysinmedicine.symptomImmunosuppressive AgentsHumanmedicine.medical_specialtyAngioimmunoblastic T-cell lymphomaPopulationHigh endothelial venulesDendritic CellLymphoma T-CellTransplantation AutologousmedicineHumanseducationCell Proliferationbusiness.industryPeripheral T-cell lymphomaDendritic Cellsmedicine.diseasePeripheral T-cell lymphomaLymphomaTransplantationImmunologyLymph NodesGeriatrics and GerontologybusinessStem Cell Transplantation
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Risk of classical Kaposi sarcoma by plasma levels of Epstein-Barr virus antibodies, sCD26, sCD23 and sCD30

2010

Abstract Background To clarify the immunological alterations leading to classical Kaposi sarcoma (cKS) among people infected with KS-associated herpesvirus (KSHV). Methods In a population-based study of 119 cKS cases, 105 KSHV-seropositive controls, and 155 KSHV-seronegative controls, we quantified plasma soluble cluster of differentiation (sCD) levels and antibodies against Epstein-Barr virus nuclear antigen-1 (anti-EBNA-1) and viral capsid antigen (anti-VCA). Differences between groups in prevalence of low-tertile anti-EBNA-1 and high-tertile anti-VCA were compared by logistic regression. Continuous levels between groups and by presence of cKS co-factors among controls were compared by li…

Cancer ResearchEpidemiologyPopulationmedicine.disease_causeSettore MED/42 - Igiene Generale E Applicatalcsh:RC254-282Viruslcsh:Infectious and parasitic diseasesDiabetes mellitusmedicinelcsh:RC109-216educationeducation.field_of_studyEpstein-Barr virus antibodiebiologyCluster of differentiationbusiness.industryKaposi sarcomasCD26 sCD23 and sCD30lcsh:Neoplasms. Tumors. Oncology. Including cancer and carcinogensmedicine.diseaseEpstein–Barr virusInfectious DiseasesOncologyImmunologyKaposi sarcoma; Epstein-Barr virus antibodies; sCD26 sCD23 and sCD30biology.proteinSarcomaCortisoneAntibodybusinessmedicine.drugResearch ArticleInfectious Agents and Cancer
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Impact of infectious burden on progression of carotid atherosclerosis.

2002

Background and Purpose— Recent findings suggest a causative role of infections in the pathogenesis of atherosclerosis. The extent of atherosclerosis and the prognosis of patients with atherosclerosis seem to be increased by the number of infections to which an individual has been exposed. In a prospective study, we evaluated the effect of 8 pathogens and the aggregate pathogen burden on the progression of carotid atherosclerosis. Methods— In 504 patients (74.9% men; age, 62.9±10 years), we measured intima-media thickness and prevalence of carotid artery stenosis. Follow-up measurements after a mean of 2.5 years were available in 427 patients (85%). Blood samples were taken, and IgG or IgA …

Carotid Artery DiseasesMalemedicine.medical_specialtyMycoplasma pneumoniaePathologyEpstein-Barr Virus InfectionsStatinHaemophilus Infectionsmedicine.drug_classComorbiditymedicine.disease_causeAntibodies ViralInfectionsGastroenterologyVirusHelicobacter InfectionsSeroepidemiologic StudiesInternal medicineGermanymedicineOdds RatioPrevalenceHumansMycoplasma InfectionsProspective StudiesProspective cohort studyChlamydophila InfectionsUltrasonographyAdvanced and Specialized NursingChlamydiaVascular diseasebusiness.industryHerpes SimplexOdds ratioMiddle Agedmedicine.diseaseAntibodies BacterialImmunoglobulin AHerpes simplex virusCarotid ArteriesImmunoglobulin GCytomegalovirus InfectionsDisease ProgressionFemaleNeurology (clinical)Cardiology and Cardiovascular MedicinebusinessTunica IntimaTunica MediaStroke
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Can persistent Epstein-Barr virus infection induce Chronic Fatigue Syndrome as a Pavlov reflex of the immune response?

2012

Chronic Fatigue Syndrome is a protracted illness condition (lasting even years) appearing with strong flu symptoms and systemic defiances by the immune system. Here, by means of statistical mechanics techniques, we study the most widely accepted picture for its genesis, namely a persistent acute mononucleosis infection, and we show how such infection may drive the immune system toward an out-of-equilibrium metastable state displaying chronic activation of both humoral and cellular responses (a state of full inflammation without a direct "causes-effect" reason). By exploiting a bridge with a neural scenario, we mirror killer lymphocytes $T_K$ and $B$ cells to neurons and helper lymphocytes $…

Cytotoxicity ImmunologicEpstein-Barr Virus InfectionsHerpesvirus 4 HumanMononucleosisT-LymphocytesFOS: Physical sciencesInflammationBiologyVirusimmunologyImmune systemAntigenEpstein-Barr Virus InfectionCell Behavior (q-bio.CB)medicineChronic fatigue syndromeHumansimmunology; statistical mechanicsEpstein–Barr virus infectionEcology Evolution Behavior and SystematicsCondensed Matter - Statistical MechanicsB-LymphocytesFatigue Syndrome ChronicEcologyStatistical Mechanics (cond-mat.stat-mech)B-LymphocyteImmunitymedicine.diseasePhysics - Medical PhysicsFOS: Biological sciencesImmunologyReflexQuantitative Biology - Cell Behaviorstatistical mechanicsMedical Physics (physics.med-ph)medicine.symptomImmunologic MemoryHuman
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