Search results for "congé"

showing 10 items of 33 documents

Achados orais na síndrome de williams-beuren

2017

Background: Williams-Beuren syndrome (WBS; OMIM #194050) is a developmental disorder characterized by congenital heart disease, intellectual disability, dysmorphic facial features and ophthalmologic abnormalities. Oral abnormalities are also described in clinical manifestations of the disease. This paper describes orofacial features in patients with WBS. Material and Methods: Seventeen patients with a confirmed molecular diagnosis of WBS were examined for oral abnormalities through clinical oral evaluations and panoramic radiography. Results: Malocclusion, specifically with dental midline deviation, and high-arched palate were the most common findings. Conclusions: The present results contr…

0301 basic medicineAdultMaleWilliams SyndromeSíndrome de Williams-BeurenPediatricsmedicine.medical_specialtycongenital hereditary and neonatal diseases and abnormalitiesHeart diseaseAdolescentAnomalias congénitasDiseaseOdontologiaCongenital abnormalities03 medical and health sciencesYoung Adult0302 clinical medicineQuality of lifeWilliams-Beuren syndromeIntellectual disabilitymedicineHumansAbnormalities Multiplecardiovascular diseasesYoung adultChildGeneral DentistryOral Medicine and Pathologybusiness.industryTooth AbnormalitiesResearch030206 dentistrymedicine.disease:CIENCIAS MÉDICAS [UNESCO]oral featuresDevelopmental disorderCaracterísticas orofaciaisstomatognathic diseases030104 developmental biologyOtorhinolaryngologyChild PreschoolUNESCO::CIENCIAS MÉDICASSurgeryFemaleWilliams syndromeMalocclusionbusinessMalocclusionMedicina oral, patologia oral y cirugia bucal
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International BEAT-PCD Consensus Statement for Infection Prevention and Control for Primary Ciliary Dyskinesia in collaboration with ERN-LUNG PCD Cor…

2021

Introduction In primary ciliary dyskinesia (PCD) impaired mucociliary clearance leads to recurrent airway infections and progressive lung destruction, and concern over chronic airway infection and patient-to-patient transmission is considerable. So far, there has been no defined consensus on how to control infection across centres caring for patients with PCD. Within the BEAT-PCD network, COST Action and ERS CRC together with the ERN-Lung PCD core a first initiative has now been taken towards creating such a consensus statement. Methods A multidisciplinary international PCD expert panel was set up to create a consensus statement for infection prevention and control (IP&C) for PCD, covering …

:Otros calificadores::Otros calificadores::/prevención & control [Otros calificadores]Infeccions respiratòries en els infantsPrimary Ciliary DyskinesiaStatement (logic)Respiratory SystemMULTICENTERRECOMMENDATIONS0302 clinical medicineOriginal Research ArticlesPandemicSTENOTROPHOMONAS-MALTOPHILIAInfection control:Pathological Conditions Signs and Symptoms::Pathologic Processes::Disease Attributes::Chronic Disease [DISEASES]030212 general & internal medicinePrimary ciliary dyskinesiaMalalties transmissibles - Transmissió:Environmental Health::Health::Environmental Illness::Communicable Diseases::Communicable Disease Control [PUBLIC HEALTH]FOUNDATIONbiologyTransmission (medicine)R:Congenital Hereditary and Neonatal Diseases and Abnormalities::Congenital Abnormalities::Abnormalities Multiple::Ciliopathies::Congenital Hereditary and Neonatal Diseases and Abnormalities::Ciliary Motility Disorders [DISEASES]:afecciones patológicas signos y síntomas::procesos patológicos::atributos de la enfermedad::enfermedad crónica [ENFERMEDADES]:salud ambiental::salud::enfermedad ambiental::enfermedades transmisibles::control de enfermedades transmisibles [SALUD PÚBLICA]medicine.anatomical_structureMedicinePatient representativesLife Sciences & BiomedicinePulmonary and Respiratory Medicinemedicine.medical_specialty3610 Medicine & health:enfermedades y anomalías neonatales congénitas y hereditarias::anomalías congénitas::anomalías múltiples::ciliopatías::enfermedades y anomalías neonatales congénitas y hereditarias::trastornos de la motilidad ciliar [ENFERMEDADES]:Other subheadings::Other subheadings::/prevention & control [Other subheadings]03 medical and health sciencesotorhinolaryngologic diseasesmedicineIntensive care medicineScience & TechnologyCYSTIC-FIBROSISLungbusiness.industryPSEUDOMONAS-AERUGINOSAMalalties cròniques - PrevencióCAREEFFICACYmedicine.diseasebiology.organism_classificationrespiratory tract diseases030228 respiratory systemNontuberculous mycobacteria610 Medizin und GesundheitbusinessERJ Open Research
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Le droit au congé individuel de formation au prisme des territoires

2008

08031; À travers une étude qualitative menée auprès de trois FONGECIF et une analyse économétrique des candidatures et bénéficiaires d'un congé individuel de formation (CIF), cette communication tente d'appréhender les différents usages du CIF, de cerner les conditions de sélection des dossiers, afin de souligner les risques d'inégalités territoriales dans l'accès des salariés à ce droit individuel.

Congé Individuel de Formation[SHS.SOCIO]Humanities and Social Sciences/Sociology[SHS.SOCIO] Humanities and Social Sciences/Sociology[SHS.EDU]Humanities and Social Sciences/Education[SHS.EDU] Humanities and Social Sciences/EducationInégalité territorialeSélectionTerritoire[ SHS.EDU ] Humanities and Social Sciences/Education[ SHS.SOCIO ] Humanities and Social Sciences/SociologyDroit à la formation
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Organisation comparée, un ou des FONGECIF ?

2008

08076

Congé individuel de formationDroitFONGECIF[SHS.EDU]Humanities and Social Sciences/EducationFormation professionnelle continue[SHS.EDU] Humanities and Social Sciences/Education[ SHS.EDU ] Humanities and Social Sciences/Education
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Un droit à géométrie variable

1995

International audience; Les dernières statistiques le confirment : ce n'est pas dans les entreprises où la formation est la plus développée que les efforts accomplis sont le mieux rémunérés. Reste que mieux vaut toujours être jeune, qualifié, de sexe masculin et employé dans une grande entreprise de haute technologie pour pouvoir bénéficier d'actions de formation.

Congé individuel de formationEntreprise[SHS.EDU]Humanities and Social Sciences/EducationFormation professionnelle continueInégalité[SHS.EDU] Humanities and Social Sciences/EducationTrajectoire professionnelleAccès à la formation continueFrance
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Heurs et malheurs des demandeurs de CIF

2008

08077

Congé individuel de formationFONGECIF[SHS.EDU]Humanities and Social Sciences/Education[SHS.EDU] Humanities and Social Sciences/EducationFinancement[ SHS.EDU ] Humanities and Social Sciences/Education
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Structure du marché du travail, formation continue et trajectoires professionnelles : l'exemple du congé individuel de formation

1992

séminaire coorganisé par le Centre d'études et de recherches sur les qualifications, CEREQ et le Laboratoire d'analyse secondaire et de méthodes appliquées à la sociologie, LASMAS] \par "Mobilité professionnelle et cheminement de longue durée", janvier 1991 - mars 1992; International audience

Congé individuel de formation[SHS.EDU]Humanities and Social Sciences/EducationFormation professionnelle continue[SHS.EDU] Humanities and Social Sciences/EducationTrajectoire professionnelleStructureFranceMarché du travail
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Le statut de l'avocat collaborateur libéral suite aux États généraux de l'avenir de la profession

2019

International audience

Contrat de Collaboration LibéraleCongé paternité[SHS.DROIT]Humanities and Social Sciences/Law[SHS.DROIT] Humanities and Social Sciences/LawComputingMilieux_MISCELLANEOUSDroit à la déconnexion
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Presenting signs and patient co-variables in Gaucher disease: outcome of the Gaucher Earlier Diagnosis Consensus (GED-C) Delphi initiative.

2019

Background: Gaucher disease (GD) presents with a range of signs and symptoms. Physicians can fail to recognise the early stages of GD owing to a lack of disease awareness, which can lead to significant diagnostic delays and sometimes irreversible but avoidable morbidities. Aim: The Gaucher Earlier Diagnosis Consensus (GED-C) initiative aimed to identify signs and co-variables considered most indicative of early type 1 and type 3 GD, to help non-specialists identify ‘at-risk’ patients who may benefit from diagnostic testing. Methods: An anonymous, three-round Delphi consensus process was deployed among a global panel of 22 specialists in GD (median experience 17.5 years, collectively managin…

Delphi TechniqueDisease outcomethrombocytopeniaMedicina Clínica030204 cardiovascular system & hematology0302 clinical medicine//purl.org/becyt/ford/3.2 [https]Lysosomal storage disease030212 general & internal medicinecomputer.programming_languageGaucher Malaltia de:Ciencias de la información::análisis de sistemas::técnica Delfos [CIENCIA DE LA INFORMACIÓN]lysosomal storage diseaseINBORN ERROR:Information Science::Systems Analysis::Delphi Technique [INFORMATION SCIENCE]Original Article//purl.org/becyt/ford/3 [https]Corrigendum:Diagnosis::Early Diagnosis [ANALYTICAL DIAGNOSTIC AND THERAPEUTIC TECHNIQUES AND EQUIPMENT]medicine.medical_specialtyCIENCIAS MÉDICAS Y DE LA SALUDSPLENOMEGALYConsensusPrognosiLYSOSOMAL STORAGE DISEASEMETABOLISMinborn error03 medical and health sciencesPhysiciansInternal MedicinemedicineHumansHematologíaALGORITHM:enfermedades del sistema nervioso::enfermedades del sistema nervioso central::enfermedades cerebrales::enfermedades cerebrales metabólicas::enfermedades cerebrales metabólicas congénitas::enfermedades por almacenamiento lisosómico del sistema nervioso::esfingolipidosis::enfermedad de Gaucher [ENFERMEDADES]splenomegalyalgorithmGaucher Diseasebusiness.industryTHROMBOCYTOPENIA:Nervous System Diseases::Central Nervous System Diseases::Brain Diseases::Brain Diseases Metabolic::Brain Diseases Metabolic Inborn::Lysosomal Storage Diseases Nervous System::Sphingolipidoses::Gaucher Disease [DISEASES]Original Articlesmedicine.disease:diagnóstico::diagnóstico precoz [TÉCNICAS Y EQUIPOS ANALÍTICOS DIAGNÓSTICOS Y TERAPÉUTICOS]Early DiagnosisFamily medicinebusinessmetabolismcomputerDelphiInternal medicine journal
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[Drugs use in pregnancy in the Valencia Region and the risk of congenital anomalies].

2017

Background Despite the potential risks of drug use during pregnancy, consumption has increased in recent decades. Objective To identify the risk of congenital anomalies (CA) associated with the use of drugs in primary care in pregnant women resident in the Valencia Region. Methods A case-control study, considering a case as a less than one year old live birth in 2009–2010, diagnosed with a CA and resident in the Valencia Region, obtained from the CA population-based registry. Controls were selected from the Metabolic Disease Registry, and the drugs prescribed and dispensed from the Integral Management of Pharmaceutical Services. Crude odds ratio (OR) was calculated with its 95% confidence i…

DrugAdultMalemedicine.medical_specialtyPreparación farmacéuticaEmbarazomedia_common.quotation_subjectPopulationLogistic regressionPediatricsRJ1-570Comunitat Valenciana03 medical and health sciencesYoung Adult0302 clinical medicinePregnancyRisk FactorsManagement of Technology and InnovationInternal medicineAmbulatory CareMedicineAnomalías congénitasHumans030212 general & internal medicineeducationmedia_commonPregnancyeducation.field_of_study030219 obstetrics & reproductive medicinebusiness.industryInfant NewbornAbnormalities Drug-InducedOdds ratioDexketoprofenmedicine.diseaseConfidence intervalSurgeryPregnancy ComplicationsSpainCase-Control StudiesFemalebusinessLive birthmedicine.drugFactores de riesgoAnales de pediatria (Barcelona, Spain : 2003)
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