Oxidative stress and mitochondrial dysfunction in Kindler syndrome

6533b833fe1ef96bd129c302

RESEARCH PRODUCT

Oxidative stress and mitochondrial dysfunction in Kindler syndrome

Sara Guerrero-aspizua Federico Pallardó Marcela Del Rio Cristina Has Elisabeth Zapatero-solana José Manuel García-verdugo Fernando Larcher Agustí Toll Jelena Markovic José Luis García-giménez Claudio J. Conti Eulalia Baselga Marta García Maria Duran-moreno

subject

Premature aging Male Keratinocytes Adolescent ComputingMilieux_LEGALASPECTSOFCOMPUTING Mitochondrion medicine.disease_cause Pathogenesis Kindler syndrome 03 medical and health sciences chemistry.chemical_compound 0302 clinical medicine Blister medicine Humans Genetics(clinical)Pharmacology (medical)Photosensitivity Disorders Genodermatosis Child Genetics (clinical)Cells Cultured Periodontal Diseases 030304 developmental biology Aged 80 and over Medicine(all)0303 health sciences integumentary system Research General Medicine Glutathione Middle Aged medicine.disease Malondialdehyde Molecular biology 3. Good health Mitochondria Oxidative Stress chemistry Oxidative stress 030220 oncology & carcinogenesis Child Preschool Female Skin cancer Epidermolysis Bullosa Kindlin1 Oxidative stress

description

This is an Open Access article distributed under the terms of the Creative Commons Attribution License.-- et al.

year	journal	country	edition	language
2014-01-01	Orphanet Journal of Rare Diseases

10.1186/s13023-014-0211-8 http://dx.doi.org/10.1186/s13023-014-0211-8

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