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RESEARCH PRODUCT
Congenital Cystic Lesions of the Bile Ducts: Imaging-Based Diagnosis
Mariangela DiamarcoGiuseppe CutaiaMassimo MidiriDario GiambellucaRoberto CannellaGiovanni CaruanaGiuseppe Salvaggiosubject
Liver Cirrhosismedicine.medical_specialtyCaroli diseaseDigestive System DiseasesHamartomaCystic lesions030218 nuclear medicine & medical imagingDiagnosis Differential03 medical and health sciencesCystic lesion0302 clinical medicineMedicineHumansRadiology Nuclear Medicine and imagingCholedochal cystsFibropolycystic liver diseasemedicine.diagnostic_testbusiness.industryCystsPolycystic liver diseaseLiver DiseasesUltrasoundGenetic Diseases InbornMagnetic resonance imagingmedicine.diseaseCaroli DiseaseLiver030220 oncology & carcinogenesisCongenital hepatic fibrosisRadiologyDifferential diagnosisbusinessSettore MED/36 - Diagnostica Per Immagini E Radioterapiadescription
Congenital cystic lesions of the bile ducts represent a spectrum of liver and biliary system lesions, resulting from abnormal embryologic development of the ductal plate. These disorders include Caroli disease, choledochal cysts, autosomal dominant polycystic liver disease, congenital hepatic fibrosis, and biliary hamartomas. Each disorder carries a peculiar clinical presentation, prognosis, and risk of complications. Knowledge of radiological findings of fibropolycystic liver diseases is crucial for their appropriate detection and for differential diagnosis with other similar hepatic cystic lesions, in order to avoid relevant misdiagnosis. The aim of this review is to provide an illustrative summary of the most relevant imaging findings of these conditions as encountered on ultrasound, computed tomography, and magnetic resonance imaging, and provide pearls for imaging-based differential diagnosis. (c) 2019 Elsevier Inc. All rights reserved.
| year | journal | country | edition | language |
|---|---|---|---|---|
| 2020-07-01 |