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RESEARCH PRODUCT

Beckwith-Wiedemann Syndrome: Open bite evolution after tongue reduction

Jesús-manuel MuñozJ. Hernández-godoyMercedes MartínEstefanía Alonso-rodríguezMiguel BurgueñoElena Gómez

subject

MaleBeckwith-Wiedemann SyndromeAdolescentmedicine.medical_treatmentOral Surgical ProceduresBeckwith–Wiedemann syndromeReviewDrooling03 medical and health sciences0302 clinical medicineTonguemedicineMacroglossiaHumansPhonationChildGeneral DentistryReduction (orthopedic surgery)Retrospective StudiesOrthodonticsbusiness.industryOpen BiteInfantRetrospective cohort study030206 dentistryAirway obstruction:CIENCIAS MÉDICAS [UNESCO]medicine.diseaseTreatment OutcomeOtorhinolaryngologyChild Preschool030220 oncology & carcinogenesisUNESCO::CIENCIAS MÉDICASGlossectomyFemaleSurgeryOral Surgerymedicine.symptombusiness

description

Background Macroglossia causes functional deficits such as airway obstruction, drooling, phonation difficulties, and leads to protrusion of dentoalveolar structures resulting in an anterior open bite and a prognathic mandibular appearance. Macroglossia is present in the majority of patients with Beckwith-Wiedemann syndrome (BWS) and surgical treatment may be indicated. Material and Methods A retrospective review was conducted including BWS patients who underwent surgical tongue reduction between 2000 and 2015 at the Hospital Universitario La Paz, Madrid. Results Out of 16 patients with BWS, surgery was performed in 11 cases. Tongue protrusion with open bite was the main indication for surgical treatment. Reduction glossectomy was performed using the keyhole technique. We analysed the relationship between age at surgery and evolution of open bite. Complications were minimal and satisfactory outcomes were observed with a decrease in anterior open bite. Conclusions In this study we have observed that surgical treatment in patients with BWS and open bite accompanied by macroglossia seems to provide positive results with a satisfactory outcome in dentoskeletal alterations. Key words:Macroglossia, Beckwith- Wiedemann syndrome, glossectomy; tongue reduction, malocclusion.

yearjournalcountryeditionlanguage
2018-02-01Medicina Oral Patología Oral y Cirugia Bucal
https://doi.org/10.4317/medoral.21319