6533b85bfe1ef96bd12ba883

RESEARCH PRODUCT

Adaptation to Disease and Anxiety-Depressive Clinic in the Paediatric Patient with Primary Ciliary Dyskinesia

subject

description

Introduction: Primary ciliary dyskinesia is a rare, autosomal recessive disease of low prevalence in paediatrics. Studies in psychology have not analysed the role of family-psychological variables in rare diseases such as primary ciliary dyskinesia. Objectives: this study aims to analyse the presence of clinical anxiety-depressive and perception threat of disease in patients with dyskinesia and evaluate the adaptation to the disease. Material-Methods: All patients with primary ciliary dyskinesia (9 to 18 years of age), attended in the Infantile Pneumology Unit of HCUV, from July 2015 to January 2019, who accepted to complete the Anxiety Depression (HADS) and Perception of Disease Threat (BIP-Q) questionnaires, have been included. Outcomes are evaluated according to treatment and the presence of bronchiectasis. Results: 12 patients were included (75% of patients had bronchiectasis, 44.4% were varicose, 44.4 cylindrical and 11.1% both). Fifty percent received nebulized treatment and 83.3% inhaled aerosol therapy. 41.9% presented anxious symptoms and 16.7% of the subjects presented a clinical problem of depression and a tendency to underestimate the threat of the disease. Conclusions: A high percentage of patients with dyskinesia suffer symptoms of anxiety and underestimate their illness, so it is important for them to adopt measures to detect risk factors for mental health, develop protocols for psychological action for cases that require it and increase the number of studies addressing this issue.