Search results for "Synaptic Vesicles"

showing 10 items of 26 documents

TBC1D24-TLDc-related epilepsy exercise-induced dystonia: rescue by antioxidants in a disease model

2019

Genetic mutations in TBC1D24 have been associated with multiple phenotypes, with epilepsy being the main clinical manifestation. The TBC1D24 protein consists of the unique association of a Tre2/Bub2/Cdc16 (TBC) domain and a TBC/lysin motif domain/catalytic (TLDc) domain. More than 50 missense and loss-of-function mutations have been described and are spread over the entire protein. Through whole genome/exome sequencing we identified compound heterozygous mutations, R360H and G501R, within the TLDc domain, in an index family with a Rolandic epilepsy exercise-induced dystonia phenotype (http://omim.org/entry/608105). A 20-year long clinical follow-up revealed that epilepsy was self-limited in…

MaleModels Molecular0301 basic medicineProtein ConformationAmino Acid Motifsalpha-TocopherolMutantCrystallography X-RayPHENOTYPECompound heterozygosityAntioxidantsAnimals Genetically ModifiedEpilepsy0302 clinical medicineCatalytic DomainDrosophila ProteinsMissense mutationoxidative stressChildTLDC DOMAINVITAMIN-EExome sequencingSequence DeletionNeuronsDystoniaGeneticsexercise-induced dystoniaTBC1D24GTPase-Activating ProteinsANNOTATIONSEpilepsy RolandicPhenotypeRecombinant ProteinsPedigree3. Good healthRolandic epilepsyDystoniaDrosophila melanogasterChild PreschoolFemaleSettore MED/26 - NeurologiaSynaptic VesiclesDrosophila melanogasterPROTEIN STABILITYLife Sciences & BiomedicineLocomotionAdolescentPhysical ExertionMutation MissenseClinical NeurologyPREDICTIONSBiology03 medical and health sciencesmedicineAnimalsHumansAmino Acid SequenceCOMPARTMENToxidative streScience & TechnologySequence Homology Amino AcidMUTATIONSNeurosciencesInfantBiological TransportDEGRADATIONmedicine.diseasebiology.organism_classificationAcetylcysteineDisease Models AnimalOxidative Stress030104 developmental biologyrab GTP-Binding ProteinsSEIZURESNeurosciences & NeurologyNeurology (clinical)Reactive Oxygen SpeciesSequence Alignment030217 neurology & neurosurgery
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Strain differences in the ratio of synaptic body types in photoreceptors of the rat retina.

1993

In the retinal outer plexiform layer of seven different rat strains, synaptic bodies (SB) were counted and, according to their morphology, characterized as synaptic ribbons (SR), synaptic spheres (SS) or intermediate structures. It was found that absolute SB numbers showed relatively small variations while SR/SS ratios differed considerably between the strains investigated. These results are discussed with respect to retinal pigmentation and to formation and degradation, respectively, of synaptic ribbons.

MaleMorphology (linguistics)Outer plexiform layerlaw.inventionSynapsechemistry.chemical_compoundSpecies SpecificitylawmedicineAnimalsPhotoreceptor CellsSynaptic ribbonRetinaStrain (chemistry)PigmentationRetinalRats Inbred StrainsSensory SystemsRatsOphthalmologyMicroscopy Electronmedicine.anatomical_structurechemistryBiophysicsFemalesense organsSynaptic VesiclesElectron microscopeNeuroscienceVision research
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Synaptic vesicle alterations in rod photoreceptors of synaptophysin-deficient mice.

2001

Abstract The abundance of the integral membrane protein synaptophysin in synaptic vesicles and its multiple possible functional contributions to transmitter exocytosis and synaptic vesicle formation stand in sharp contrast to the observed lack of defects in synaptophysin knockout mice. Assuming that deficiencies are compensated by the often coexpressed synaptophysin isoform synaptoporin, we now show that retinal rod photoreceptors, which do not synthesize synaptoporin either in wild-type or in knockout mice, are affected by the loss of synaptophysin. Multiple pale-appearing photoreceptors, as seen by electron microscopy, possess reduced cytoplasmic electron density, swollen mitochondria, an…

MalePresynaptic TerminalsSynaptophysinAction PotentialsFluorescent Antibody TechniqueDark AdaptationBiologyRibbon synapseSynaptic vesicleSynaptic TransmissionExocytosisExocytosisMiceRetinal Rod Photoreceptor CellsElectroretinographySynaptic vesicle recyclingAnimalsMice KnockoutSex CharacteristicsGeneral NeuroscienceVesicleMembrane ProteinsClathrin-Coated VesiclesSynaptoporinCell biologyMice Inbred C57BLMicroscopy ElectronProtein TransportKnockout mouseSynaptophysinbiology.proteinFemaleSynaptic VesiclesNeurosciencePhotic StimulationNeuroscience
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Ultrastructural observations on the central innervation of the guinea-pig pineal gland.

1981

In the present study the central innervation of the guinea-pig pineal gland was investigated. The habenulae and the pineal stalk contain myelinated and non-myelinated nerve fibres with few dense-cored and electron-lucent vesicles. Some myelinated fibres leave the main nerve fibre bundles, lose their myelin-sheaths and terminate in the pineal gland. Although direct proof is lacking, the non-myelinated fibres appear to end near the site where the bulk of the myelinated fibres are located. Here a neuropil area exists where synapses between non-myelinated fibre elements are abundant. Neurosecretory fibres were also seen. The results support the concept of functional interrelationships between h…

Maleendocrine systemCytoplasmHistologyGuinea PigsBiologySynaptic vesicleNerve Fibers MyelinatedPineal GlandPathology and Forensic MedicineGuinea pigPineal glandNerve FibersEpendymamedicineNeuropilEpithalamusAnimalsCell NucleusCell BiologyAnatomyMicroscopy Electronmedicine.anatomical_structurenervous systemHypothalamusSynapsesUltrastructureSynaptic VesiclesEpendymahormones hormone substitutes and hormone antagonistsCell and tissue research
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In vitro effects of putative neurotransmitters on synaptic ribbon numbers and N-acetyltransferase activity in the rat pineal gland

1992

The pineal contains a large number of classical transmitters and neuropeptides. Some of these neurochemicals are involved in the regulation of serotonin N-acetyltransferase (NAT) activity and hence in melatonin synthesis. Synaptic ribbons present in the pineal gland also exhibit a numerical day/night rhythm parallel to that of NAT activity. There is scarcity of information regarding the regulation of synaptic ribbon (SR) numbers. In the present study, we have investigated in vitro effects of a number of classical neurotransmitters and neuropeptides. NAT activity was used to monitor melatonin synthesis under the experimental conditions used. Norepinephrine (NE), Delta sleep-inducing peptide …

Maleendocrine systemmedicine.medical_specialtyArylamine N-AcetyltransferaseVasoactive intestinal peptideNeuropeptideBiologyPineal Glandgamma-Aminobutyric acidRats Sprague-DawleyPineal glandOrgan Culture TechniquesInternal medicinemedicineAnimalsBiological PsychiatrySynaptic ribbonNeurotransmitter AgentsfungiCircadian RhythmRatsbody regionsMicroscopy ElectronPsychiatry and Mental healthmedicine.anatomical_structureEndocrinologySomatostatinNeurologySynaptic VesiclesNeurology (clinical)Serotoninhormones hormone substitutes and hormone antagonistsmedicine.drugEndocrine glandJournal of Neural Transmission
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"Synaptic" ribbons and spherules of the rat pineal gland: day/night changes in vitro?

1982

In the present study pineal glands of rats aged 69–71 days were studied in vivo and in vitro with respect to day/night changes of “synaptic” ribbons and spherules. It was found that ribbons outnumber spherules by a factor of 3. In vivo, both ribbons and spherules show a roughly 3-fold increase in number at 1 a.m. when compared to 1 p.m. Up to 39 h in vitro, the two structures in question did not reveal day/night differences in amount, suggesting that diurnal rhythmicity of the gland did apparently not persist in organ culture. After 3 h in organ culture, the spherules, but not the ribbons, showed a striking increase in number, showing that ribbons and spherules may be governed by different …

Malemedicine.medical_specialtyGeneral NeuroscienceSynaptic MembranesRats Inbred StrainsBiologyOrgan culturePineal GlandIn vitroCircadian RhythmRatsRat Pineal GlandPineal glandMicroscopy Electronmedicine.anatomical_structureEndocrinologynervous systemIn vivoInternal medicineSynapsesmedicineAnimalssense organsSynaptic VesiclesExperimental brain research
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Investigations on day-night differences of vesicle densities in synapses of the rat suprachiasmatic nucleus

1990

The present study was conducted to test whether the well-known circadian alterations in physiological and metabolical parameters of the hypothalamic suprachiasmatic nucleus (SCN) are accompanied by day-night differences in the number of vesicles in intrinsic synapses of the nucleus. Two groups of 5 adult male rats each were killed at mid-light or mid-dark, respectively, by perfusion with Karnovsky's fluid. The SCN were removed and processed for routine electron microscopy. In medial parts of the nucleus, synapses were characterized as being of Gray type I (asymmetrical), Gray type II (symmetrical) or of intermediate form, and the vesicles per synaptic profile (VPSP) were counted over a defi…

Malephotoperiodismmedicine.medical_specialtySuprachiasmatic nucleusGeneral NeuroscienceVesicleRats Inbred StrainsBiologySynaptic vesicleAxonsCircadian RhythmRatsSynapseMicroscopy ElectronEndocrinologymedicine.anatomical_structureHypothalamusInternal medicineSynapsesmedicineAnimalsSuprachiasmatic NucleusSynaptic VesiclesCircadian rhythmNucleusNeuroscience Letters
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Zinc-positive presynaptic boutons of the rabbit hippocampus during early postnatal development

1998

Abstract The evolution of vesicular zinc-containing boutons in the developing rabbit hippocampus has been studied during early postnatal life using the selenite–Danscher histochemical method. By P3, large immature mossy fiber boutons with labeled synaptic vesicles were seen in the hilus of the dentate gyrus and in the stratum lucidum of the CA3–CA4 hippocampal areas. After P5, smaller boutons with labeled vesicles were identified in the stratum oriens and stratum radiatum of all hippocampal areas, and even transiently in the stratum lacunosum of P6 animals. Vesicular zinc-containing boutons increased in number and underwent ultrastructural maturation; light microscope densitometric–volumetr…

Mossy fiber (hippocampus)medicine.medical_specialtyPresynaptic TerminalsHippocampusHippocampal formationBiologyHippocampusSynaptic vesiclelaw.inventionNerve FibersDevelopmental NeurosciencelawInternal medicinemedicineAnimalsDentate gyrusAnatomyZincmedicine.anatomical_structureEndocrinologyAnimals Newbornnervous systemDentate GyrusUltrastructureRegression AnalysisRabbitsSynaptic VesiclesElectron microscopeDevelopmental BiologyStratum lucidumDevelopmental Brain Research
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Transcriptome comparison of murine wild-type and synaptophysin-deficient retina reveals complete identity

2005

Loss of synaptophysin, one of the major synaptic vesicle membrane proteins, is surprisingly well tolerated in knockout mice. To test whether compensatory gene transcription accounts for the apparent lack of functional deficiencies, comparative transcriptome analyses were carried out. The retina was selected as the most suitable tissue since morphological alterations were observed in mutant photoreceptors, most notably a reduction of synaptic vesicles and concomitant increase in clathrin-coated vesicles. Labeled cRNA was prepared in triplicate from retinae of age- and sex-matched wild-type and mutant litter mates and hybridized to high-density microarray chips. Only three differentially expr…

MutantSynaptophysinSynaptic vesicleRetinaTranscriptomeMiceMicroscopy Electron TransmissionGene expressionAnimalsPhotoreceptor CellsRNA MessengerEye ProteinsMolecular BiologyMice KnockoutbiologyReverse Transcriptase Polymerase Chain ReactionSynaptic vesicle membraneGeneral NeuroscienceWild typeGlucan 13-beta-GlucosidaseMicroarray AnalysisMolecular biologyClathrinMice Inbred C57BLGene Expression RegulationKnockout mouseSynaptophysinbiology.proteinSynaptic VesiclesNeurology (clinical)Developmental BiologyBrain Research
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Synaptogenesis in the mouse olfactory bulb during glomerulus development

2008

Synaptogenesis is essential for the development of neuronal networks in the brain. In the olfactory bulb (OB) glomeruli, numerous synapses must form between sensory olfactory neurons and the dendrites of mitral/tufted and periglomerular cells. Glomeruli develop from E13 to E16 in the mouse, coincident with an increment of the neuropil in the border between the external plexiform (EPL) and olfactory nerve layers (ONL), coupled to an extensive labelling of phalloidin and GAP-43 from the ONL to EPL. We have tracked synaptogenesis in the OB during this period by electron microscopy (EM) and immunolabelling of the transmembrane synaptic vesicle glycoprotein SV-2. No SV-2 labelling or synapses we…

Olfactory systemNeuropilTime FactorsPhalloidineSynaptic MembranesSynaptogenesisGAP-43Nerve Tissue ProteinsBiologymitral cellsSynaptic TransmissionOlfactory Receptor NeuronsMiceGAP-43 ProteinOlfactory MucosaOlfactory nerveolfactory sensory neuronsNeuropilmedicineAnimalsGlomerulus (olfaction)Membrane GlycoproteinsGeneral NeuroscienceSV-2Cell DifferentiationDendritesOlfactory BulbOlfactory bulbmedicine.anatomical_structureSynapsesembryonic structuresSynaptic VesiclesOlfactory ensheathing gliaolfactory epitheliumsense organsNeuroscienceOlfactory epitheliumBiomarkers
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