6533b837fe1ef96bd12a3131

RESEARCH PRODUCT

205th ENMC International Workshop: Pathology diagnosis of idiopathic inflammatory myopathies Part II 28-30 March 2014, Naarden, The Netherlands.

subject

description

The idiopathic inflammatory myopathies (IM) are a heterogeneous group of diseases and diagnosis often necessitates a muscle biopsy. Five main entities are recognized: (1) dermatomyositis (DM); (2) polymyositis (PM); (3) necrotizing autoimmune myopathy (NAM); (4) sporadic inclusion body myositis (IBM); and (5) non-specific myositis. Other entities include granulomatous myopathy, macrophagic myofasciitis, and eosinophilic fasciitis (Shulman's syndrome). The pathological classification and subsequent identification of disease subgroups are extremely important for assessing treatment options and prognosis in the individual patient, yet classification criteria have not been standardized and validated. The 193rd ENMC Workshop on the Pathologic Diagnosis of Idiopathic Inflammatory Myopathies was held in 2012, in order to establish guidelines for a standardized diagnostic work up. This 205th ENMC International Workshop brought together 20 experts with significant expertise in muscle biopsy reading from suspected IM patients from 11 countries from various parts of the world: Australia, Belgium, Denmark, France, Germany, Japan, The Netherlands, Sweden, Switzerland, the United Kingdom, and the United States of America.